Preferred Label : Granulomatosis with Polyangiitis;

MeSH definition : A multisystemic disease of a complex genetic background. It is characterized by inflammation of the blood vessels (VASCULITIS) leading to damage in any number of organs. The common features include granulomatous inflammation of the RESPIRATORY TRACT and KIDNEYS. Most patients have measurable autoantibodies (ANTINEUTROPHIL CYTOPLASMIC ANTIBODIES) against MYELOBLASTIN.;

MeSH synonym : granulomatosis, wegener's; granulomatosis, wegener; wegener's granulomatosis; Granulomatosis with Polyangiitides; Polyangiitides, Granulomatosis with; Polyangiitis, Granulomatosis with; with Polyangiitides, Granulomatosis; with Polyangiitis, Granulomatosis; Wegener Granulomatosis;

CISMeF synonym : Wegener;

Wikipedia link : https://en.wikipedia.org/wiki/Granulomatosis with polyangiitis;

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A multisystemic disease of a complex genetic background. It is characterized by inflammation of the blood vessels (VASCULITIS) leading to damage in any number of organs. The common features include granulomatous inflammation of the RESPIRATORY TRACT and KIDNEYS. Most patients have measurable autoantibodies (ANTINEUTROPHIL CYTOPLASMIC ANTIBODIES) against MYELOBLASTIN.

https://www.medg.fr/granulomatose-avec-polyangeite
2018
France
teaching material
scientific and technical information
Granulomatosis with Polyangiitis
systemic vasculitis
Granulomatosis
granulomatosis, nos

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https://www.medg.fr/granulomatose-a-eosinophiles-avec-polyangeite
2018
France
teaching material
scientific and technical information
granulomatosis, nos
eosinophilia, nos
Granulomatosis with Polyangiitis
eosinophilia
Granulomatosis
systemic vasculitis
eosinophils
Eosinophilia
eosinophil

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http://www.snfmi.org/content/granulomatose-avec-polyang%C3%A9ite-maladie-de-wegener
2014
false
true
false
false
France
French
popular works
Granulomatosis with Polyangiitis
Granulomatosis with Polyangiitis
Granulomatosis with Polyangiitis
Granulomatosis with Polyangiitis
Granulomatosis with Polyangiitis
Granulomatosis with Polyangiitis
Granulomatosis with Polyangiitis

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http://www.dermis.net/dermisroot/fr/25316/diagnose.htm
Germany
French
Granulomatosis with Polyangiitis
diagnosis, differential
image

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http://www.association-vascularites.org/
false
France
French
Granulomatosis with Polyangiitis
vasculitis
association of patients

---
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=102248
2011
France
scientific and technical information
Granulomatosis with Polyangiitis
wegener's granulomatosis
child
Granulomatosis with Polyangiitis

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http://www.has-sante.fr/portail/jcms/c_1015717/avis-de-la-has-sur-la-prise-en-charge-derogatoire-se-rapportant-aux-maladies-rares-vascularites-ald-21
2010
France
French
corticosteroid therapy
methotrexate
contraception
drug approval
immunosuppressive agents
mycophenolic acid
mycophenolic acid
rare diseases
systemic necrotizing angiitis
polyarteritis nodosa
chronic disease
aspirin
Granulomatosis with Polyangiitis
churg-strauss syndrome
Off-Label use
microscopic polyangiitis
acetylsalicylic acid lysinate
lysine
aspirin
-
administration, oral
ischemia
platelet aggregation inhibitors
anti-inflammatory agents, non-steroidal
chlormadinone acetate
contraceptives, oral, synthetic
guidelines for drug use
drug evaluation

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http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=900
http://www.orpha.net/data/patho/FR/fr-wegener.pdf
2007
true
France
French
Granulomatosis with Polyangiitis
Granulomatosis with Polyangiitis
Granulomatosis with Polyangiitis
Granulomatosis with Polyangiitis
scientific and technical information
handbooks

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http://www.orpha.net/data/patho/Pub/fr/Wegener-FRfrPub759v01.pdf
2007
France
French
Granulomatosis with Polyangiitis
rare diseases
Granulomatosis with Polyangiitis
signs and symptoms
Granulomatosis with Polyangiitis
activities of daily living
patient education handout

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http://www.has-sante.fr/portail/display.jsp?id=c_608145
http://www.has-sante.fr/portail/display.jsp?id=c_608140
http://www.has-sante.fr/portail/jcms/c_717292/fr/ald-n-21-sclerodermie-generalisee-evolutive
2007
true
France
French
child
pregnancy
adult
polyarteritis nodosa
Granulomatosis with Polyangiitis
churg-strauss syndrome
vasculitis, leukocytoclastic, cutaneous
continuity of patient care
polyarteritis nodosa
Granulomatosis with Polyangiitis
vasculitis, leukocytoclastic, cutaneous
churg-strauss syndrome
practice guideline

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29/05/2024


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