" /> Granulomatosis with Polyangiitis - CISMeF





Preferred Label : Granulomatosis with Polyangiitis;

NCIt synonyms : Wegener's Granulomatosis; Wegener s Granulomatosis; GPA; Wegener Granulomatosis;

NCIt definition : A rare, autoimmune, systemic medium and small size vasculitis. It is characterized by the formation of necrotizing granulomas in the respiratory tract, necrotizing angiitis, and glomerulonephritis.;

Alternative definition : NICHD: Systemic vasculitis affecting small to medium-sized vessels, characterized by necrotizing granulomas in the respiratory tract, necrotizing angiitis, glomerulonephritis with little to no immune complex deposition, and typically positive for antineutrophil cytoplasmic antibody staining in a cytoplasmic pattern (C-ANCA; antiproteinase 3).;

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28/07/2025


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