Granulomatosis with Polyangiitis

Preferred Label : Granulomatosis with Polyangiitis;

NCIt synonyms : Wegener's Granulomatosis; Wegener s Granulomatosis; GPA; Wegener Granulomatosis;

NCIt definition : A rare, autoimmune, systemic medium and small size vasculitis. It is characterized by the formation of necrotizing granulomas in the respiratory tract, necrotizing angiitis, and glomerulonephritis.;

Alternative definition : NICHD: Systemic vasculitis affecting small to medium-sized vessels, characterized by necrotizing granulomas in the respiratory tract, necrotizing angiitis, glomerulonephritis with little to no immune complex deposition, and typically positive for antineutrophil cytoplasmic antibody staining in a cytoplasmic pattern (C-ANCA; antiproteinase 3).;

Details

Origin ID

C3444;

UMLS CUI

C3495801;

Automatic exact mappings (from CISMeF team)
- Glycophorin a [OMIM gene]
- surrogate mothers [MeSH Descriptor]
Currated CISMeF NLP mapping
- Granulomatosis with Polyangiitis [MeSH Descriptor]
- Granulomatosis with Polyangiitis [MeSH concept]
- Granulomatosis with polyangiitis [MedDRA Preferred Term]
- Granulomatosis with polyangiitis [ICD-11 Sub-sub category]
- Granulomatosis with polyangiitis [Radlex concept]
- Granulomatosis with polyangiitis [OMIM Phenotype]
- Granulomatosis with polyangiitis [ORDO Disease]
- Granulomatosis with polyangiitis (disorder) [SNOMED CT concept]
- Granulomatous polyangiitis [MedDRA LLT]
- WEGENER'S GRANULOMATOSIS [WHO-ART Preferred Term]
- Wegener granulomatosis [PASCAL descriptor]
- Wegener granulomatosis [ACR pathology]
- Wegener granulomatosis [ACR pathology]
- Wegener granulomatosis [Disease (Nov.)]
- Wegener's granulomatosis [ICD-9 code]
- Wegener's granulomatosis [ICD-10 Sub-category]
- Wegener's granulomatosis [MedDRA LLT]
- Wegeners granulomatosis [ICD-10 Sub-category (who)]
- Wegeners granulomatosis [MedDRA LLT]
- granulomatosis with polyangiitis [DO Concept]
- granulomatosis with polyangiitis [MedlinePlus Topic]
- wegener's granulomatosis [SNOMED Notion]
DO Cross reference
- granulomatosis with polyangiitis [DO Concept]
Has associated anatomic sites
- Cardiovascular System [NCIt concept]
- Vascular System [NCIt concept]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Granulomatosis with Polyangiitis [MeSH Descriptor]
- Granulomatosis with polyangiitis [MedDRA Preferred Term]
- Granulomatosis with polyangiitis [OMIM Phenotype]
- Granulomatosis with polyangiitis [ORDO Disease]
- Granulomatosis with polyangiitis [Radlex concept]
- Granulomatosis with polyangiitis [ICD-11 Sub-sub category]
- Granulomatosis with polyangiitis (disorder) [SNOMED CT concept]
- Granulomatous polyangiitis [MedDRA LLT]
- WEGENER'S GRANULOMATOSIS [WHO-ART Preferred Term]
- Wegener granulomatosis [PASCAL descriptor]
- Wegener granulomatosis [ACR pathology]
- Wegener granulomatosis [ACR pathology]
- Wegener granulomatosis [Disease (Nov.)]
- Wegener's granulomatosis [ICD-9 code]
- Wegener's granulomatosis [ICD-10 Sub-category]
- Wegener's granulomatosis [MedDRA LLT]
- Wegeners granulomatosis [MedDRA LLT]
- granulomatosis with polyangiitis [MedlinePlus Topic]
- granulomatosis with polyangiitis [DO Concept]
- wegener's granulomatosis [SNOMED Notion]
associated_with_malfunction_of_gene_product
- Myeloblastin [NCIt concept]
concept_is_in_subset
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]
- NICHD Terminology [NCIt concept]
- Pediatric Rheumatology Terminology [NCIt concept]
disease_has_finding
- Rare Lesion [NCIt concept]

Keyword's position in hierarchy(ies) :

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