ICD-11 code : 4A44.A1;
Preferred Label : Granulomatosis with polyangiitis;
ICD-11 definition : Necrotizing granulomatous inflammation usually involving the upper and lower respiratory
tract, and necrotizing vasculitis affecting predominantly small to medium-sized vessels
(e.g., capillaries, venules, arterioles, arteries and veins). Necrotizing glomerulonephritis
is common . (Arthritis Rheum 1990;33:1101-1107);
ICD-11 synonym : Wegener granulomatosis;
ICD-11 inclusion : Necrotising respiratory granulomatosis; Wegener granulomatosis;
Origin ID : 1020056159;
UMLS CUI : C3495801;
Currated CISMeF NLP mapping
ICD-10 Mapping
Semantic type(s)
UMLS correspondences (same concept)
Validated automatic mappings to BTNT
Necrotizing granulomatous inflammation usually involving the upper and lower respiratory
tract, and necrotizing vasculitis affecting predominantly small to medium-sized vessels
(e.g., capillaries, venules, arterioles, arteries and veins). Necrotizing glomerulonephritis
is common . (Arthritis Rheum 1990;33:1101-1107)