" /> Granulomatosis with polyangiitis - CISMeF





ICD-11 code : 4A44.A1;

Preferred Label : Granulomatosis with polyangiitis;

ICD-11 definition : Necrotizing granulomatous inflammation usually involving the upper and lower respiratory tract, and necrotizing vasculitis affecting predominantly small to medium-sized vessels (e.g., capillaries, venules, arterioles, arteries and veins). Necrotizing glomerulonephritis is common . (Arthritis Rheum 1990;33:1101-1107);

ICD-11 synonym : Wegener granulomatosis;

ICD-11 inclusion : Necrotising respiratory granulomatosis; Wegener granulomatosis;

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Necrotizing granulomatous inflammation usually involving the upper and lower respiratory tract, and necrotizing vasculitis affecting predominantly small to medium-sized vessels (e.g., capillaries, venules, arterioles, arteries and veins). Necrotizing glomerulonephritis is common . (Arthritis Rheum 1990;33:1101-1107)

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03/05/2025


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