Preferred Label : churg-strauss syndrome;
MeSH definition : Widespread necrotizing angiitis with granulomas. Pulmonary involvement is frequent.
Asthma or other respiratory infection may precede evidence of vasculitis. Eosinophilia
and lung involvement differentiate this disease from POLYARTERITIS NODOSA.;
MeSH synonym : vasculitis, churg-strauss; syndrome, churg-strauss; granulomatous angiitides, allergic; angiitis, allergic granulomatous; granulomatous angiitis, allergic; churg-strauss vasculitis; vasculitis, churg strauss; allergic granulomatous angiitis; allergic granulomatous angiitides; angiitides, allergic granulomatous; allergic angiitis; allergic angiitides; angiitides, allergic; angiitis, allergic; churg strauss syndrome; allergic angiitis and granulomatosis; allergic granulomatosis; allergic granulomatoses; granulomatoses, allergic; granulomatosis, allergic; allergic granulomatous and angiitis; eosinophilic granulomatous vasculitis; granulomatous vasculitides, eosinophilic; granulomatous vasculitis, eosinophilic; vasculitides, eosinophilic granulomatous; vasculitis, eosinophilic granulomatous; granulomatous allergic angiitis; allergic angiitides, granulomatous; allergic angiitis, granulomatous; angiitides, granulomatous allergic; angiitis, granulomatous allergic; granulomatous allergic angiitides; EGPA Disorder; Disorder, EGPA; Disorders, EGPA; EGPA Disorders; Eosinophilic Granulomatosis with Polyangiitis;
CISMeF synonym : Churg-Strauss; churg-strauss's syndrome; eosinophilic granulomatous vasculitides;
Wikipedia link : https://en.wikipedia.org/wiki/Allergic granulomatosis;
Origin ID : D015267;
UMLS CUI : C0008728;
Allowable qualifiers
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
DO Cross reference
False automatic mappings
Manual NTBT mappings (CISMeF)
MedlinePlus topic(s)
ORDO relation(s)
Record concept(s)
Semantic type(s)
UMLS correspondences (same concept)
Validated automatic mappings to NTBT
Widespread necrotizing angiitis with granulomas. Pulmonary involvement is frequent.
Asthma or other respiratory infection may precede evidence of vasculitis. Eosinophilia
and lung involvement differentiate this disease from POLYARTERITIS NODOSA.
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=183
http://www.orpha.net/data/patho/Pro/fr/ChurgStrauss-FRfrPro745.pdf
2020
true
France
French
churg-strauss syndrome
churg-strauss syndrome
churg-strauss syndrome
scientific and technical information
---
http://www.has-sante.fr/portail/jcms/c_1015717/avis-de-la-has-sur-la-prise-en-charge-derogatoire-se-rapportant-aux-maladies-rares-vascularites-ald-21
2010
France
French
corticosteroid therapy
methotrexate
contraception
drug approval
immunosuppressive agents
mycophenolic acid
mycophenolic acid
rare diseases
systemic necrotizing angiitis
polyarteritis nodosa
chronic disease
aspirin
Granulomatosis with Polyangiitis
churg-strauss syndrome
Off-Label use
microscopic polyangiitis
acetylsalicylic acid lysinate
lysine
aspirin
-
administration, oral
ischemia
platelet aggregation inhibitors
anti-inflammatory agents, non-steroidal
chlormadinone acetate
contraceptives, oral, synthetic
guidelines for drug use
drug evaluation
---
http://www.has-sante.fr/portail/display.jsp?id=c_608145
http://www.has-sante.fr/portail/display.jsp?id=c_608140
http://www.has-sante.fr/portail/jcms/c_717292/fr/ald-n-21-sclerodermie-generalisee-evolutive
2007
true
France
French
child
pregnancy
adult
polyarteritis nodosa
Granulomatosis with Polyangiitis
churg-strauss syndrome
vasculitis, leukocytoclastic, cutaneous
continuity of patient care
polyarteritis nodosa
Granulomatosis with Polyangiitis
vasculitis, leukocytoclastic, cutaneous
churg-strauss syndrome
practice guideline
---
http://www.orpha.net/data/patho/Pub/fr/ChurgStrauss-FRfrPub745v01.pdf
2007
true
France
French
churg-strauss syndrome
churg-strauss syndrome
patient education handout
hotlines
---