Preferred Label : churg-strauss syndrome;

MeSH definition : Widespread necrotizing angiitis with granulomas. Pulmonary involvement is frequent. Asthma or other respiratory infection may precede evidence of vasculitis. Eosinophilia and lung involvement differentiate this disease from POLYARTERITIS NODOSA.;

MeSH synonym : vasculitis, churg-strauss; syndrome, churg-strauss; granulomatous angiitides, allergic; angiitis, allergic granulomatous; granulomatous angiitis, allergic; churg-strauss vasculitis; vasculitis, churg strauss; allergic granulomatous angiitis; allergic granulomatous angiitides; angiitides, allergic granulomatous; allergic angiitis; allergic angiitides; angiitides, allergic; angiitis, allergic; churg strauss syndrome; allergic angiitis and granulomatosis; allergic granulomatosis; allergic granulomatoses; granulomatoses, allergic; granulomatosis, allergic; allergic granulomatous and angiitis; eosinophilic granulomatous vasculitis; granulomatous vasculitides, eosinophilic; granulomatous vasculitis, eosinophilic; vasculitides, eosinophilic granulomatous; vasculitis, eosinophilic granulomatous; granulomatous allergic angiitis; allergic angiitides, granulomatous; allergic angiitis, granulomatous; angiitides, granulomatous allergic; angiitis, granulomatous allergic; granulomatous allergic angiitides; EGPA Disorder; Disorder, EGPA; Disorders, EGPA; EGPA Disorders; Eosinophilic Granulomatosis with Polyangiitis;

CISMeF synonym : Churg-Strauss; churg-strauss's syndrome; eosinophilic granulomatous vasculitides;

Wikipedia link : https://en.wikipedia.org/wiki/Allergic granulomatosis;

Details


Main resources

You can consult :

Widespread necrotizing angiitis with granulomas. Pulmonary involvement is frequent. Asthma or other respiratory infection may precede evidence of vasculitis. Eosinophilia and lung involvement differentiate this disease from POLYARTERITIS NODOSA.

http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=183
http://www.orpha.net/data/patho/Pro/fr/ChurgStrauss-FRfrPro745.pdf
2020
true
France
French
churg-strauss syndrome
churg-strauss syndrome
churg-strauss syndrome
scientific and technical information

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http://www.has-sante.fr/portail/jcms/c_1015717/avis-de-la-has-sur-la-prise-en-charge-derogatoire-se-rapportant-aux-maladies-rares-vascularites-ald-21
2010
France
French
corticosteroid therapy
methotrexate
contraception
drug approval
immunosuppressive agents
mycophenolic acid
mycophenolic acid
rare diseases
systemic necrotizing angiitis
polyarteritis nodosa
chronic disease
aspirin
Granulomatosis with Polyangiitis
churg-strauss syndrome
Off-Label use
microscopic polyangiitis
acetylsalicylic acid lysinate
lysine
aspirin
-
administration, oral
ischemia
platelet aggregation inhibitors
anti-inflammatory agents, non-steroidal
chlormadinone acetate
contraceptives, oral, synthetic
guidelines for drug use
drug evaluation

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http://www.has-sante.fr/portail/display.jsp?id=c_608145
http://www.has-sante.fr/portail/display.jsp?id=c_608140
http://www.has-sante.fr/portail/jcms/c_717292/fr/ald-n-21-sclerodermie-generalisee-evolutive
2007
true
France
French
child
pregnancy
adult
polyarteritis nodosa
Granulomatosis with Polyangiitis
churg-strauss syndrome
vasculitis, leukocytoclastic, cutaneous
continuity of patient care
polyarteritis nodosa
Granulomatosis with Polyangiitis
vasculitis, leukocytoclastic, cutaneous
churg-strauss syndrome
practice guideline

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http://www.orpha.net/data/patho/Pub/fr/ChurgStrauss-FRfrPub745v01.pdf
2007
true
France
French
churg-strauss syndrome
churg-strauss syndrome
patient education handout
hotlines

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26/05/2025


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