ICD-11 code : 4A44.A2;
Preferred Label : Eosinophilic granulomatosis with polyangiitis;
ICD-11 definition : Eosinophil-rich and necrotizing granulomatous inflammation often involving the respiratory
tract, and necrotizing vasculitis predominantly affecting small to medium-sized vessels,
and associated with asthma and eosinophilia. ANCA is most frequent when glomerulonephritis
is present. (Arthritis Rheum 1990;33:1094-1100);
ICD-11 synonym : Churg-Strauss syndrome; Allergic granulomatous angiitis; Churg-Strauss vasculitis;
ICD-11 inclusion : Churg-Strauss syndrome;
Origin ID : 835880885;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
Eosinophil-rich and necrotizing granulomatous inflammation often involving the respiratory
tract, and necrotizing vasculitis predominantly affecting small to medium-sized vessels,
and associated with asthma and eosinophilia. ANCA is most frequent when glomerulonephritis
is present. (Arthritis Rheum 1990;33:1094-1100)