idiopathic pulmonary fibrosis

Preferred Label : idiopathic pulmonary fibrosis;

MeSH definition : A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.;

MeSH synonym : cryptogenic fibrosing alveolitis; fibrosing alveolitides, cryptogenic; pulmonary fibroses, idiopathic; idiopathic pulmonary fibroses; pulmonary fibrosis, idiopathic; cryptogenic fibrosing alveolitides; fibrosing alveolitis, cryptogenic; fibrocystic pulmonary dysplasia; dysplasia, fibrocystic pulmonary; fibrocystic pulmonary dysplasias; pulmonary dysplasia, fibrocystic; idiopathic fibrosing alveolitis, chronic form;

CISMeF synonym : Hamman-Rich disease; Hamman-Rich diseases; disease, Hamman-Rich; diseases, Hamman-Rich; dysplasias, fibrocystic pulmonary; familial idiopathic pulmonary fibrosis; hamman rich disease; interstitial pneumonias, usual; interstitial pneumonitides, usual; pulmonary dysplasias, fibrocystic; usual interstitial pneumonia;

CISMeF acronym : IPF;

MeSH hyponym : Idiopathic Pulmonary Fibrosis, Familial;

Related MeSH term : Interstitial Pneumonia, Usual; Usual Interstitial Pneumonias; Interstitial Pneumonitis, Usual; Pneumonitides, Usual Interstitial; Pneumonitis, Usual Interstitial; Usual Interstitial Pneumonitides; Usual Interstitial Pneumonitis;

MeSH annotation : do not confuse with PULMONARY FIBROSIS; PULMONARY FIBROSIS is also available;

Wikipedia link : https://en.wikipedia.org/wiki/Idiopathic pulmonary fibrosis;

Details

Origin ID

D054990;

UMLS CUI

C1800706;

Allowable qualifiers
- blood [MeSH Qualifier]
- cerebrospinal fluid [MeSH Qualifier]
- chemically induced [MeSH Qualifier]
- classification [MeSH Qualifier]
- complications [MeSH Qualifier]
- congenital [MeSH Qualifier]
- diagnosis [MeSH Qualifier]
- diagnostic imaging [MeSH Qualifier]
- diet therapy [MeSH Qualifier]
- drug therapy [MeSH Qualifier]
- economics [MeSH Qualifier]
- embryology [MeSH Qualifier]
- enzymology [MeSH Qualifier]
- epidemiology [MeSH Qualifier]
- ethnology [MeSH Qualifier]
- etiology [MeSH Qualifier]
- genetics [MeSH Qualifier]
- history [MeSH Qualifier]
- immunology [MeSH Qualifier]
- metabolism [MeSH Qualifier]
- microbiology [MeSH Qualifier]
- mortality [MeSH Qualifier]
- nursing [MeSH Qualifier]
- parasitology [MeSH Qualifier]
- pathology [MeSH Qualifier]
- physiopathology [MeSH Qualifier]
- prevention and control [MeSH Qualifier]
- psychology [MeSH Qualifier]
- radiotherapy [MeSH Qualifier]
- rehabilitation [MeSH Qualifier]
- surgery [MeSH Qualifier]
- therapy [MeSH Qualifier]
- urine [MeSH Qualifier]
- veterinary [MeSH Qualifier]
- virology [MeSH Qualifier]
Automatic exact mappings (from CISMeF team)
- Idiopathic fibrosing alveolitis, chronic form (disorder) [Inactive SNOMED CT concept]
- Immature Platelets to Total Platelets Ratio Measurement [NCIt concept]
- Usual Interstitial Pneumonia [NCIt concept]
- Usual interstitial pneumonia [HPO term]
- acute interstitial pneumonia [DO Concept]
- idiopathic interstitial pneumonia [DO Concept]
Currated CISMeF NLP mapping
- ALVEOLITIS FIBROSING [WHO-ART Preferred Term]
- Alveolitis fibrosing [MedDRA LLT]
- Cryptogenic fibrosing alveolitis [MedDRA LLT]
- Diffuse interstitial pulmonary fibrosis (disorder) [SNOMED CT concept]
- Fibrosing alveolitis [MedDRA LLT]
- Fibrosing alveolitis (idiopathic) [MedDRA LLT]
- Idiopathic Pulmonary Fibrosis [NCIt concept]
- Idiopathic pulmonary fibrosis [ICD-11 Subcategory]
- Idiopathic pulmonary fibrosis [MedDRA Preferred Term]
- Idiopathic pulmonary fibrosis [ICD-9 code]
- Idiopathic pulmonary fibrosis [ORDO Disease]
- Idiopathic pulmonary fibrosis (disorder) [SNOMED CT concept]
- idiopathic fibrosing alveolitis, chronic form [SNOMED Notion]
- idiopathic pulmonary fibrosis [DO Concept]
- idiopathic pulmonary fibrosis [Disease (Nov.)]
- idiopathic pulmonary fibrosis [Radlex concept]
- pulmonary fibrosis [MedlinePlus Topic]
DO Cross reference
- idiopathic pulmonary fibrosis [DO Concept]
Has phenotype(s) (HPO)
- Increased alveolar cell carcinoma [HPO term]
Manual NTBT mappings (CISMeF)
- Idiopathic interstitial pneumonia [ORDO Disease]
- Rare pulmonary hypertension [ORDO Disease]
ORDO relation(s)
- Idiopathic pulmonary fibrosis [ORDO Disease]
Record concept(s)
- Familial Idiopathic Pulmonary Fibrosis [MeSH concept]
- Usual Interstitial Pneumonia [MeSH concept]
- idiopathic pulmonary fibrosis [MeSH concept]
See also (suggested by CISMeF)
- macitentan [MeSH Supplementary Concept]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- ALVEOLITIS FIBROSING [WHO-ART Preferred Term]
- Alveolitis fibrosing [MedDRA LLT]
- Cryptogenic fibrosing alveolitis [MedDRA LLT]
- Familial idiopathic pulmonary fibrosis (disorder) [SNOMED CT concept]
- Fibrosing alveolitis [MedDRA LLT]
- Fibrosing alveolitis (idiopathic) [MedDRA LLT]
- Idiopathic Pulmonary Fibrosis [NCIt concept]
- Idiopathic fibrosing alveolitis, chronic form (disorder) [Inactive SNOMED CT concept]
- Idiopathic pulmonary fibrosis [MedDRA Preferred Term]
- Idiopathic pulmonary fibrosis [ORDO Disease]
- Idiopathic pulmonary fibrosis [ICD-9 code]
- Idiopathic pulmonary fibrosis (disorder) [SNOMED CT concept]
- Interstitial lung disease 2 [OMIM Phenotype]
- Usual Interstitial Pneumonia [NCIt concept]
- idiopathic pulmonary fibrosis [DO Concept]
- idiopathic pulmonary fibrosis [Disease (Nov.)]
- idiopathic pulmonary fibrosis [Radlex concept]
Validated automatic mappings to BTNT
- Chronic idiopathic pulmonary fibrosis (disorder) [SNOMED CT concept]
- Familial idiopathic pulmonary fibrosis (disorder) [SNOMED CT concept]
- Interstitial lung disease 2 [OMIM Phenotype]
Validated automatic mappings to NTBT
- Other interstitial pulmonary diseases with fibrosis [ICD-10 Sub-category (who)]

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