Idiopathic pulmonary fibrosis

ICD-11 code : CB03.4;

Preferred Label : Idiopathic pulmonary fibrosis;

ICD-11 definition : Idiopathic pulmonary fibrosis (IPF) is defined as a specific form of chronic, progressive fibrosing interstitial pneumonia (pneumonitis) of unknown cause, occurring primarily in older adults, limited to the lungs, and associated with the histopathologic and/or radiologic pattern of UIP. The definition of IPF requires the exclusion of other forms of interstitial pneumonia (pneumonitis) including other idiopathic interstitial pneumonias (pneumonitis) and Interstitial Lung Disease (ILD) associated with environmental exposure, medication, or systemic disease.;

ICD-11 synonym : fibrosing pneumonitis; pulmonary fibrosis NOS; fibrosing lung disease; idiopathic lung fibrosis; fibrosing alveolitis; interstitial pulmonary fibrosis; IPF - [Idiopathic pulmonary fibrosis];

ICD-11 acronym : IPF;

Details

Origin ID

1074069640;

UMLS CUI

C0034069;

Automatic exact mappings (from CISMeF team)
- Immature Platelets to Total Platelets Ratio Measurement [NCIt concept]
- Interstitial lung fibrosis [MedDRA LLT]
- Interstitial pulmonary fibrosis [MedDRA LLT]
- Lung fibrosis interstitial [MedDRA LLT]
- idiopathic interstitial pneumonia [DO Concept]
Currated CISMeF NLP mapping
- ALVEOLITIS FIBROSING [WHO-ART Preferred Term]
- Abnormal pulmonary interstitial morphology [HPO term]
- Alveolitis fibrosing [MedDRA LLT]
- Diffuse interstitial pulmonary fibrosis (disorder) [SNOMED CT concept]
- Fibrosing alveolitis [MedDRA LLT]
- Fibrosis of lung (disorder) [SNOMED CT concept]
- Idiopathic Pulmonary Fibrosis [NCIt concept]
- Idiopathic pulmonary fibrosis [ORDO Disease]
- Idiopathic pulmonary fibrosis [ICD-9 code]
- Idiopathic pulmonary fibrosis [MedDRA Preferred Term]
- Idiopathic pulmonary fibrosis (disorder) [SNOMED CT concept]
- Interstitial lung disease 2 [OMIM Phenotype]
- Pulmonary Fibrosis [NCIt concept]
- idiopathic pulmonary fibrosis [MeSH Descriptor]
- idiopathic pulmonary fibrosis [Radlex concept]
- idiopathic pulmonary fibrosis [DO Concept]
- idiopathic pulmonary fibrosis [MeSH concept]
- pulmonary fibrosis [MedlinePlus Topic]
- pulmonary fibrosis [MeSH Descriptor]
ICD-10 Mapping
- Other interstitial pulmonary diseases with fibrosis [ICD-10 Sub-category]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Fibrosis lung [MedDRA LLT]
- Fibrosis of lung (disorder) [SNOMED CT concept]
- Fibrosis pulmonary [MedDRA LLT]
- Lung fibrosis [MedDRA LLT]
- Lung fibrosis [HRDO Sign]
- PULMONARY FIBROSIS [WHO-ART Preferred Term]
- Pneumosclerosis [MedDRA LLT]
- Pulmonary Fibrosis [NCIt concept]
- Pulmonary fibrosis [HPO term]
- Pulmonary fibrosis [LOINC component]
- Pulmonary fibrosis [MedDRA Preferred Term]
- Pulmonary fibrosis [PASCAL descriptor]
- fibrosis of lung, nos [SNOMED Notion]
- lung fibrosis [Disease (Nov.)]
- pulmonary fibrosis [DO Concept]
- pulmonary fibrosis [MedlinePlus Topic]
- pulmonary fibrosis [MeSH Descriptor]
- pulmonary fibrosis [MeSH concept]

Keyword's position in hierarchy(ies) :

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