Idiopathic Pulmonary Fibrosis

Preferred Label : Idiopathic Pulmonary Fibrosis;

NCIt synonyms : IPF;

NCIt definition : Chronic and progressive fibrosis of the lung parenchyma of unknown cause.;

Alternative definition : NCI-GLOSS: A disease in which the alveoli (tiny air sacs at the end of the bronchioles in the lungs) are overgrown with fibrous tissue. The cause of the disease is unknown and it gets worse over time. Symptoms include difficult, painful breathing and shortness of breath.;

Codes from synonyms : CDR0000648991;

Details

Origin ID

C35716;

UMLS CUI

C1800706;

Automatic exact mappings (from CISMeF team)
- Idiopathic fibrosing alveolitis, chronic form (disorder) [Inactive SNOMED CT concept]
- Other interstitial pulmonary diseases with fibrosis [ICD-10 Sub-category (who)]
- idiopathic interstitial pneumonia [DO Concept]
Currated CISMeF NLP mapping
- Abnormal pulmonary interstitial morphology [HPO term]
- Familial idiopathic pulmonary fibrosis (disorder) [SNOMED CT concept]
- Fibrosing alveolitis [MedDRA LLT]
- Idiopathic pulmonary fibrosis [ICD-11 Subcategory]
- Idiopathic pulmonary fibrosis [ICD-9 code]
- Idiopathic pulmonary fibrosis [MedDRA Preferred Term]
- Idiopathic pulmonary fibrosis [ORDO Disease]
- Idiopathic pulmonary fibrosis (disorder) [SNOMED CT concept]
- Interstitial lung disease 2 [OMIM Phenotype]
- idiopathic pulmonary fibrosis [DO Concept]
- idiopathic pulmonary fibrosis [Disease (Nov.)]
- idiopathic pulmonary fibrosis [MeSH Descriptor]
- idiopathic pulmonary fibrosis [MeSH concept]
- idiopathic pulmonary fibrosis [Radlex concept]
- pulmonary fibrosis [MedlinePlus Topic]
DO Cross reference
- idiopathic pulmonary fibrosis [DO Concept]
Has associated anatomic sites
- Lung [NCIt concept]
- Respiratory System [NCIt concept]
- Thoracic Cavity [NCIt concept]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- ALVEOLITIS FIBROSING [WHO-ART Preferred Term]
- Alveolitis fibrosing [MedDRA LLT]
- Cryptogenic fibrosing alveolitis [MedDRA LLT]
- Familial idiopathic pulmonary fibrosis (disorder) [SNOMED CT concept]
- Fibrosing alveolitis [MedDRA LLT]
- Fibrosing alveolitis (idiopathic) [MedDRA LLT]
- Idiopathic fibrosing alveolitis, chronic form (disorder) [Inactive SNOMED CT concept]
- Idiopathic pulmonary fibrosis [MedDRA Preferred Term]
- Idiopathic pulmonary fibrosis [ORDO Disease]
- Idiopathic pulmonary fibrosis [ICD-9 code]
- Idiopathic pulmonary fibrosis (disorder) [SNOMED CT concept]
- Interstitial lung disease 2 [OMIM Phenotype]
- idiopathic pulmonary fibrosis [DO Concept]
- idiopathic pulmonary fibrosis [Disease (Nov.)]
- idiopathic pulmonary fibrosis [Radlex concept]
- idiopathic pulmonary fibrosis [MeSH concept]
- idiopathic pulmonary fibrosis [MeSH Descriptor]
concept_is_in_subset
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]

Keyword's position in hierarchy(ies) :

Main resources

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