Preferred Label : idiopathic pulmonary fibrosis;
Definition : Pathology.—Idiopathic pulmonary fibrosis is a specific form of chronic fibrosing interstitial
pneumonia of unknown cause and is characterized by a histologic pattern of usual interstitial
pneumonia (5,64). Radiographs and CT scans.—The typical imaging findings are reticular
opacities and honeycombing, with a predominantly peripheral and basal distribution
(Fig 26). Ground-glass opacity, if present, is less extensive than reticular and honeycombing
patterns. The typical radiologic findings (65,66) are also encountered in usual interstitial
pneumonia secondary to specific causes, such as asbestos-induced pulmonary fibrosis
(asbestosis), and the diagnosis is usually one of exclusion. (See also usual interstitial
pneumonia.) [Fleischner Society];
Source : Fleischner Society;
Origin ID : RID28836;
UMLS CUI : C1800706;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
Semantic type(s)
UMLS correspondences (same concept)
Pathology.—Idiopathic pulmonary fibrosis is a specific form of chronic fibrosing interstitial
pneumonia of unknown cause and is characterized by a histologic pattern of usual interstitial
pneumonia (5,64). Radiographs and CT scans.—The typical imaging findings are reticular
opacities and honeycombing, with a predominantly peripheral and basal distribution
(Fig 26). Ground-glass opacity, if present, is less extensive than reticular and honeycombing
patterns. The typical radiologic findings (65,66) are also encountered in usual interstitial
pneumonia secondary to specific causes, such as asbestos-induced pulmonary fibrosis
(asbestosis), and the diagnosis is usually one of exclusion. (See also usual interstitial
pneumonia.) [Fleischner Society]