" /> idiopathic pulmonary fibrosis - CISMeF





Preferred Label : idiopathic pulmonary fibrosis;

Definition : Pathology.—Idiopathic pulmonary fibrosis is a specific form of chronic fibrosing interstitial pneumonia of unknown cause and is characterized by a histologic pattern of usual interstitial pneumonia (5,64). Radiographs and CT scans.—The typical imaging findings are reticular opacities and honeycombing, with a predominantly peripheral and basal distribution (Fig 26). Ground-glass opacity, if present, is less extensive than reticular and honeycombing patterns. The typical radiologic findings (65,66) are also encountered in usual interstitial pneumonia secondary to specific causes, such as asbestos-induced pulmonary fibrosis (asbestosis), and the diagnosis is usually one of exclusion. (See also usual interstitial pneumonia.) [Fleischner Society];

Source : Fleischner Society;

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Pathology.—Idiopathic pulmonary fibrosis is a specific form of chronic fibrosing interstitial pneumonia of unknown cause and is characterized by a histologic pattern of usual interstitial pneumonia (5,64). Radiographs and CT scans.—The typical imaging findings are reticular opacities and honeycombing, with a predominantly peripheral and basal distribution (Fig 26). Ground-glass opacity, if present, is less extensive than reticular and honeycombing patterns. The typical radiologic findings (65,66) are also encountered in usual interstitial pneumonia secondary to specific causes, such as asbestos-induced pulmonary fibrosis (asbestosis), and the diagnosis is usually one of exclusion. (See also usual interstitial pneumonia.) [Fleischner Society]

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01/05/2025


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