Preferred Label : primary myelofibrosis;
MeSH definition : A de novo myeloproliferation arising from an abnormal stem cell. It is characterized
by the replacement of bone marrow by fibrous tissue, a process that is mediated by
CYTOKINES arising from the abnormal clone.;
MeSH synonym : agnogenic myeloid metaplasias; fibroses, bone marrow; metaplasia, myeloid; metaplasias, agnogenic myeloid; myelofibroses, primary; myelofibrosis; myeloid metaplasias, agnogenic; myelosclerosis; nonleukemic myeloses; primary myelofibroses; myelofibrosis, primary; bone marrow fibrosis; bone marrow fibroses; myelosis, nonleukemic; myeloses, nonleukemic; nonleukemic myelosis; myelofibroses; myeloid metaplasia; metaplasias, myeloid; myeloid metaplasias; myeloscleroses; agnogenic myeloid metaplasia; metaplasia, agnogenic myeloid; myeloid metaplasia, agnogenic; fibrosis, bone marrow; myelofibrosis with myeloid metaplasia; idiopathic myelofibrosis; chronic idiopathic myelofibrosis;
Wikipedia link : https://en.wikipedia.org/wiki/Primary myelofibrosis;
Origin ID : D055728;
UMLS CUI : C0001815;
Allowable qualifiers
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
DO Cross reference
Manual NTBT mappings (CISMeF)
Record concept(s)
Related MeSH Supplementary Concept(s)
Semantic type(s)
UMLS correspondences (same concept)
Validated automatic mappings to NTBT
A de novo myeloproliferation arising from an abnormal stem cell. It is characterized
by the replacement of bone marrow by fibrous tissue, a process that is mediated by
CYTOKINES arising from the abnormal clone.
https://www.santepubliquefrance.fr/docs/survie-des-personnes-atteintes-de-cancer-en-france-metropolitaine-1989-2018-syndromes-myeloproliferatifs-chroniques-autres-que-leucemie-myeloide2
2021
France
technical report
myeloproliferative disorders
neoplasms
France
France
primary myelofibrosis
chronic myeloid leukemia
disease
survival
France
leukaemia
french
myeloproliferative disorders
france
France
myelofibrosis, nos
neoplasm, malignant
cancer
Chronic myelogenous leukemia
persons
leukemia, myelogenous, chronic, bcr-abl positive
---
https://www.hematocell.fr/index.php/enseignement-de-lhematologie-cellulaire/60-enseignement-de-lhematologie-cellulaire-les-principales-maladies-hematologiques/pathologie-granulocytaire-syndromes-myeloproliferatifs/106-splenomegalie-myeloide-chronique
2016
false
false
false
false
France
educational course
primary myelofibrosis
splenomegaly
primary myelofibrosis
myeloid splenomegaly
myeloid splenomegaly
---
https://hemato.chu-limoges.fr/hematolim/Portals/0/Info_patient/hemopathies/SFH/Myelofibrose_primitive.pdf
2009
false
true
false
France
popular works
primary myelofibrosis
---
https://sfh.hematologie.net/sites/sfh.hematologie.net/files/medias/documents/myelofibrose_primitive.pdf
2009
false
France
French
primary myelofibrosis
primary myelofibrosis
primary myelofibrosis
patient education handout
---