Preferred Label : mastocytosis, systemic;

MeSH definition : A group of disorders caused by the abnormal proliferation of MAST CELLS in a variety of extracutaneous tissues including bone marrow, liver, spleen, lymph nodes, and gastrointestinal tract. Systemic mastocytosis is commonly seen in adults. These diseases are categorized on the basis of clinical features, pathologic findings, and prognosis.;

MeSH synonym : systemic mast-cell disease; mast-cell disease, systemic; systemic mast-cell diseases; mastocytoses, systemic; systemic mastocytoses; systemic mastocytosis; mast-cell diseases, systemic; systemic mast cell disease;

MeSH hyponym : indolent systemic mastocytosis; aggressive systemic mastocytosis; Aggressive Systemic Mastocytoses; Mastocytoses, Aggressive Systemic; Mastocytosis, Aggressive Systemic; Systemic Mastocytoses, Aggressive; Systemic Mastocytosis, Aggressive; Indolent Systemic Mastocytoses; Mastocytoses, Indolent Systemic; Mastocytosis, Indolent Systemic; Systemic Mastocytoses, Indolent; Systemic Mastocytosis, Indolent;

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A group of disorders caused by the abnormal proliferation of MAST CELLS in a variety of extracutaneous tissues including bone marrow, liver, spleen, lymph nodes, and gastrointestinal tract. Systemic mastocytosis is commonly seen in adults. These diseases are categorized on the basis of clinical features, pathologic findings, and prognosis.

https://www.has-sante.fr/jcms/p_3359432/fr/ayvakyt-avapritinib-mastocytose-systemique-agressive-asm
https://www.has-sante.fr/jcms/p_3359458/fr/decision-n2022-0278/dc/sem-du-21-juillet-2022-du-college-de-la-haute-autorite-de-sante-portant-autorisation-d-acces-precoce-de-la-specialite-ayvakyt
2022
false
false
false
France
adult
Systemic Mastocytosis with an Associated Myeloid Neoplasm
protein kinase inhibitors
avapritinib
leukemia, mast-cell
treatment outcome
insurance, health, reimbursement
guidelines for drug use
continuity of patient care
administration, oral
evaluation of the transparency committee
avapritinib
aggressive systemic mastocytosis
mastocytosis, systemic

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http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=98850
https://www.orpha.net/data/patho/Pro/fr/Urgences_Mastocytose-frPro13309.pdf
2013
France
French
mastocytosis, systemic
emergency treatment
practice guideline
mastocytosis, systemic
aggressive systemic mastocytosis

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https://www.revmed.ch/RMS/2013/RMS-368/Allergologie2
2013
Switzerland
French
mastocytosis, systemic
journal article
mastocytosis, systemic
mastocytosis, systemic
corticosteroid therapy

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http://www.orpha.net/consor/www/cgi-bin/OC_Exp.php?lng=FR&Expert=98849
2013
France
French
practice guideline
mastocytosis, systemic
mastocytosis, systemic
emergency treatment

---
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=2467
https://www.orpha.net/data/patho/Pro/fr/Urgences_Mastocytose-frPro13309.pdf
2013
France
French
emergency treatment
practice guideline
mastocytosis, systemic
mastocytosis, systemic

---
http://www.orpha.net/consor/www/cgi-bin/OC_Exp.php?lng=FR&Expert=98848
http://www.orpha.net/data/patho/Pro/fr/Urgences_Mastocytose-frPro13309.pdf
2013
France
French
mastocytosis, systemic
mastocytosis, systemic
emergency treatment
practice guideline

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https://www.amub-ulb.be/system/files/rmb/old/792
2012
Belgium
French
mastocytosis, cutaneous
review of literature
mastocytosis, cutaneous
mastocytosis, systemic
mastocytosis, systemic
mastocytosis
mastocytosis

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18/05/2024


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