Systemic mastocytosis

ICD-11 code : 2A21.0;

Preferred Label : Systemic mastocytosis;

ICD-11 definition : Systemic mastocytosis (SM) comprises a heterogeneous group of rare acquired and chronic haematological malignancies that are related to an abnormal proliferation of mast cells in tissue, including bone marrow, with or without skin involvement. SM can be divided into indolent SM (ISM) and aggressive SM (ASM).;

ICD-11 synonym : SMCD - [systemic mast cell disease]; systemic tissue mast cell disease; systemic mast cell disease;

ICD-11 acronym : SMCD;

ICD-11 "other" category code : 2A21.0Y;

ICD-11 "unspecified" category code : 2A21.0Z;

Details

Origin ID

1144812971;

Automatic exact mappings (from CISMeF team)
- Corneal dystrophy, subepithelial mucinous [OMIM Phenotype]
- Malignant systemic mastocytosis (morphologic abnormality) [SNOMED CT concept]
- Mast cell malignancy of lymph nodes (disorder) [SNOMED CT concept]
- Mastocytosis, cutaneous [OMIM Phenotype]
- Subepithelial mucinous corneal dystrophy [ORDO Disease]
- Systemic Mastocytosis [NCIt concept]
- Systemic mast cell disease (disorder) [SNOMED CT concept]
- Systemic mastocytosis [MedDRA Preferred Term]
- Systemic mastocytosis [ORDO Disease]
- mastocytosis, systemic [MeSH Descriptor]
- mastocytosis, systemic [MeSH concept]
- subepithelial mucinous corneal dystrophy [DO Concept]
- systemic mastocytosis [DO Concept]
ICD-10 Mapping
- Malignant mast cell neoplasm [ICD-10 Sub-category]

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