Preferred Label : leukemia, mast-cell;
MeSH definition : A form of systemic mastocytosis (MASTOCYTOSIS, SYSTEMIC) characterized by the presence
of large numbers of tissue MAST CELLS in the peripheral blood without skin lesions.
It is a high-grade LEUKEMIA disease with bone marrow smear of 20% MAST CELLS, multi-organ
failure and a short survival.;
MeSH synonym : leukemias, mast-cell; mast cell leukemia; mast-cell leukemias; mast-cell leukemia; leukemia, mast cell;
Wikipedia link : https://en.wikipedia.org/wiki/Mast cell leukemia;
Origin ID : D007946;
UMLS CUI : C0023461;
- Allowable qualifiers
- Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- DO Cross reference
- False automatic mappings
- Manual NTBT mappings (CISMeF)
- ORDO relation(s)
- Record concept(s)
- Semantic type(s)
- UMLS correspondences (same concept)
A form of systemic mastocytosis (MASTOCYTOSIS, SYSTEMIC) characterized by the presence
of large numbers of tissue MAST CELLS in the peripheral blood without skin lesions.
It is a high-grade LEUKEMIA disease with bone marrow smear of 20% MAST CELLS, multi-organ
failure and a short survival.
https://www.has-sante.fr/jcms/p_3359432/fr/ayvakyt-avapritinib-mastocytose-systemique-agressive-asm
https://www.has-sante.fr/jcms/p_3359458/fr/decision-n2022-0278/dc/sem-du-21-juillet-2022-du-college-de-la-haute-autorite-de-sante-portant-autorisation-d-acces-precoce-de-la-specialite-ayvakyt
2022
false
false
false
France
adult
Systemic Mastocytosis with an Associated Myeloid Neoplasm
protein kinase inhibitors
avapritinib
leukemia, mast-cell
treatment outcome
insurance, health, reimbursement
guidelines for drug use
continuity of patient care
administration, oral
evaluation of the transparency committee
avapritinib
aggressive systemic mastocytosis
mastocytosis, systemic
---
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=FR&Expert=98851
https://www.orpha.net/data/patho/Pro/fr/Urgences_Mastocytose-frPro13309.pdf
2013
France
French
leukemia, mast-cell
emergency treatment
practice guideline
leukemia, mast-cell
---