Preferred Label : retroperitoneal fibrosis;
MeSH definition : A slowly progressive condition of unknown etiology, characterized by deposition of
fibrous tissue in the retroperitoneal space compressing the ureters, great vessels,
bile duct, and other structures. When associated with abdominal aortic aneurysm, it
may be called chronic periaortitis or inflammatory perianeurysmal fibrosis.;
MeSH synonym : disease, ormond's; ormond disease; ormond's disease; fibroses, retroperitoneal; fibrosis, retroperitoneal; retroperitoneal fibroses; disease, ormond; idiopathic retroperitoneal fibrosis;
MeSH hyponym : periaortitis, chronic; Chronic Periaortitides; Chronic Periaortitis; Periaortitides, Chronic; Fibrosis, Perianeurysmal Inflammatory; Perianeurysmal Inflammatory Fibrosis; Inflammatory Perianeurysmal Fibrosis; Perianeurysmal Fibrosis, Inflammatory; Fibrosis, Inflammatory Perianeurysmal; Inflammatory Fibrosis, Perianeurysmal;
Wikipedia link supervised : https://en.wikipedia.org/wiki/Retroperitoneal fibrosis;
Origin ID : D012185;
UMLS CUI : C0035357;
Allowable qualifiers
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
HPO term
Manual NTBT mappings (CISMeF)
ORDO relation(s)
Record concept(s)
Related MeSH Supplementary Concept(s)
See also
See also (suggested by CISMeF)
Semantic type(s)
UMLS correspondences (same concept)
Validated automatic mappings to BTNT
A slowly progressive condition of unknown etiology, characterized by deposition of
fibrous tissue in the retroperitoneal space compressing the ureters, great vessels,
bile duct, and other structures. When associated with abdominal aortic aneurysm, it
may be called chronic periaortitis or inflammatory perianeurysmal fibrosis.
http://www.snfmi.org/content/fibroses-syst%C3%A9miques
2016
false
true
false
false
France
French
popular works
retroperitoneal fibrosis
retroperitoneal fibrosis
fibrosis
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http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=49041
2006
France
French
rare diseases
retroperitoneal fibrosis
scientific and technical information
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