ICD-11 code : FB51.40;
Preferred Label : Primary retroperitoneal fibrosis;
ICD-11 definition : This is the commonest form of retroperitoneal fibrosis. By definition, no associated
trigger (e.g. drugs or malignancy) can be determined, although atherosclerosis of
the abdominal aorta is often associated. It has been postulated that such atherosclerosis
may be of aetiological significance in some cases.;
ICD-11 synonym : idiopathic retroperitoneal fibrosis;
ICD-11 inclusion : chronic periaortitis;
Origin ID : 161159769;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
This is the commonest form of retroperitoneal fibrosis. By definition, no associated
trigger (e.g. drugs or malignancy) can be determined, although atherosclerosis of
the abdominal aorta is often associated. It has been postulated that such atherosclerosis
may be of aetiological significance in some cases.
