ICD-11 code : FB51.4;
Preferred Label : Retroperitoneal fibrosis;
ICD-11 definition : Retroperitoneal fibrosis (RPF) is a disease characterised by the development of extensive
proliferation of fibrous tissue in the retroperitoneum, resulting in entrapment and
obstruction of retroperitoneal structures, notably the ureters. RPF can be classified
as primary (idiopathic) meaning that the cause is not known or secondary. But its
association with various immune-related conditions and response to immunosuppression
have led to speculation regarding an autoimmune aetiology of idiopathic RPF. One-third
of the cases are secondary to malignancy, medication, trauma, or certain infections.;
ICD-11 synonym : Ormond disease; RPF - [retroperitoneal fibrosis];
ICD-11 acronym : RPF;
ICD-11 "other" category code : FB51.4Y;
Origin ID : 967295607;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- ICD-10 Mapping
Retroperitoneal fibrosis (RPF) is a disease characterised by the development of extensive
proliferation of fibrous tissue in the retroperitoneum, resulting in entrapment and
obstruction of retroperitoneal structures, notably the ureters. RPF can be classified
as primary (idiopathic) meaning that the cause is not known or secondary. But its
association with various immune-related conditions and response to immunosuppression
have led to speculation regarding an autoimmune aetiology of idiopathic RPF. One-third
of the cases are secondary to malignancy, medication, trauma, or certain infections.
