Clear Cell Sarcoma of Soft Tissue

Preferred Label : Clear Cell Sarcoma of Soft Tissue;

NCIt synonyms : Clear Cell Sarcoma of Soft Parts; Melanoma of Soft Parts; Melanoma of the Soft Parts; Clear Cell Sarcoma of Tendons and Aponeuroses;

NCIt related terms : Melanoma, malignant, of soft parts; Clear cell sarcoma/Malignant melanoma of soft parts (excluding Clear cell sarcoma of the kidney); malignant melanoma of soft parts; Clear cell sarcoma - not kidney;

NCIt definition : A rare malignant neoplasm with melanocytic differentiation characterized by the presence of polygonal or spindle shaped clear cells. This sarcoma usually affects the tendons and aponeuroses and is associated with a poor prognosis due to recurrences and metastases.;

Alternative definition : NCI-GLOSS: A soft tissue tumor that begins in a tendon (tough, fibrous, cord-like tissue that connects muscle to bone or to another structure). Clear cell sarcoma of soft tissue has certain markers that are also found on malignant melanoma (a type of skin cancer). It usually occurs in the leg or arm.;

Neoplastic status : Malignant;

ICD-O code : 9044/3;

Codes from synonyms : CDR0000641939; 10065865; CDR0000656145;

Details

Origin ID

C3745;

UMLS CUI

C0206651;

Automatic exact mappings (from CISMeF team)
- Chordoid sarcoma [PASCAL descriptor]
- Clear cell sarcoma (except of Kidney M-89643) (morphologic abnormality) [Inactive SNOMED CT concept]
- Clear cell sarcoma of kidney [ORDO Disease]
- Clear cell sarcoma of kidney [ICD-11 Extension code]
- Clear cell sarcoma of soft tissue [MedDRA Preferred Term]
- Clear cell sarcoma, of tendons and aponeuroses [ICD-11 Extension code]
- Malignant melanoma of soft parts [ICD-11 More detail]
- Melanoma of soft tissue [ORDO Disease]
- clear cell sarcoma [DO Concept]
- kidney clear cell sarcoma [DO Concept]
- sarcoma, clear cell [MeSH Descriptor]
- sarcoma, clear cell [MeSH concept]
DO Cross reference
- clear cell sarcoma [DO Concept]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Disease may have findings
- Melanosomes Present [NCIt concept]
- Slow Growing Mass [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
False automatic mappings
- Clear cell sarcoma of kidney [ICD-O code]
- Clear cell sarcoma of kidney (morphologic abnormality) [SNOMED CT concept]
- Clear cell sarcoma of the kidney [MedDRA Preferred Term]
- clear cell sarcoma of kidney [SNOMED Notion]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Clear cell sarcoma [PASCAL descriptor]
- Clear cell sarcoma [MedDRA LLT]
- Clear cell sarcoma (except of Kidney M-89643) (morphologic abnormality) [Inactive SNOMED CT concept]
- Clear cell sarcoma (morphologic abnormality) [SNOMED CT concept]
- Clear cell sarcoma of soft tissue [MedDRA Preferred Term]
- Malignant melanoma of soft tissues (disorder) [SNOMED CT concept]
- Melanoma of soft tissue [ORDO Disease]
- clear cell sarcoma [Radlex concept]
- clear cell sarcoma [DO Concept]
- clear cell sarcoma [Disease (Nov.)]
- clear cell sarcoma (except of kidney m-89643) [SNOMED Notion]
- sarcoma, clear cell [MeSH concept]
- sarcoma, clear cell [MeSH Descriptor]
Validated automatic mappings to NTBT
- clear cell sarcoma [Disease (Nov.)]
concept_is_in_subset
- CPTAC Baseline Medical Forms Terminology [NCIt concept]
- CPTAC Sarcoma Baseline Form [NCIt concept]
- CPTAC Terminology [NCIt concept]
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCI CTEP SDC Non-Rhabdomyosarcoma Soft Tissue Sarcoma Sub-Category Terminology [NCIt concept]
- NCI CTEP Simplified Disease Classification Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Malignant Cell [NCIt concept]
- Malignant Polygonal Cell with Eosinophilic Cytoplasm [NCIt concept]
- Neoplastic Cell [NCIt concept]
disease_has_finding
- Fascicular Pattern [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- Metastatic/Recurrent Disease [NCIt concept]
- Nested Pattern [NCIt concept]
- Tissue Differentiation Uncertain [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_mapped_to_gene
- EWSR1/ATF1 Fusion Gene [NCIt concept]
- EWSR1/CREB1 Fusion Gene [NCIt concept]
disease_may_have_abnormal_cell
- Malignant Spindle Cell [NCIt concept]
- Wreath-Like Multinucleated Giant Cell [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Gain of Chromosome 7 [NCIt concept]
- Gain of Chromosome 8 [NCIt concept]
- t(12;22)(q13;q12) [NCIt concept]
- t(2;22)(q34;q12) [NCIt concept]
disease_may_have_molecular_abnormality
- EWSR1-ATF1 Fusion Protein Expression [NCIt concept]
- EWSR1-CREB1 Fusion Protein Expression [NCIt concept]
pathogenesis_of_disease_involves_gene
- EWSR1/ATF1 Fusion Gene [NCIt concept]
- EWSR1/ATF1 Fusion Gene Type 1 [NCIt concept]
- EWSR1/ATF1 Fusion Gene Type 2 [NCIt concept]
- EWSR1/CREB1 Fusion Gene [NCIt concept]

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