Preferred Label : clear cell sarcoma;
Definition : A sarcoma of young, often female, adults of the lower extremities and acral regions,
intimately bound to tendons as circumscribed but unencapsulated melanin-bearing tumors
of neuroectodermal origin. An ultrastructural finding simulates flattened and curved
barrel staves, corresponding to the internal structures of premelanosomes. There is
a 45-60% mortality in clear cell sarcoma. (Segen, Dictionary of Modern Medicine, 1992)
[MeSH];
UMLS CUI (RADLEX) : C0206651;
Origin ID : RID4557;
UMLS CUI : C0206651;
Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- Semantic type(s)
- UMLS correspondences (same concept)
A sarcoma of young, often female, adults of the lower extremities and acral regions,
intimately bound to tendons as circumscribed but unencapsulated melanin-bearing tumors
of neuroectodermal origin. An ultrastructural finding simulates flattened and curved
barrel staves, corresponding to the internal structures of premelanosomes. There is
a 45-60% mortality in clear cell sarcoma. (Segen, Dictionary of Modern Medicine, 1992)
[MeSH]
