Preferred Label : carglumic acid;
MeSH note : carglumic acid could be helpful in lowering plasma ammonia levels over 400 micromol/L
more rapidly;
CISMeF synonym : carbaglu;
Is substance : O;
UNII : 5L0HB4V1EW;
InChIKey : LCQLHJZYVOQKHU-VKHMYHEASA-N;
Origin ID : C528449;
UMLS CUI : C1318649;
ATC code(s)
CISMeF manual mappings
Exact mapping(s) to DCI
MeSH term(s) associated for indexing
Record concept(s)
See also inter- (CISMeF)
Semantic type(s)
UMLS correspondences (same concept)
Validated automatic mappings to BTNT
https://www.has-sante.fr/portail/jcms/c_2858355/fr/acide-carglumique-waymade
2018
false
false
false
false
France
French
evaluation of the transparency committee
carglumic acid
carglumic acid
acid, nos
glutamates
---
https://www.has-sante.fr/portail/jcms/c_2794115/fr/ucedane
2017
false
France
French
drugs, generic
Carglutamic acid 200mg dispersible tablet (product)
hyperammonemia
glutamates
treatment outcome
carglumic acid
carglumic acid
administration, oral
N-acetyl glutamate synthetase deficiency
amino-acid n-acetyltransferase
urea cycle disorders, inborn
propionic acidemia
Hyperammonemia due to N-acetylglutamate synthase deficiency
---
https://www.ema.europa.eu/medicines/human/EPAR/Ucedane
2017
false
United Kingdom
English
French
syndication feed
drugs, generic
Carglutamic acid 200mg dispersible tablet (product)
hyperammonemia
glutamates
treatment outcome
drug evaluation
carglumic acid
drug evaluation
summary of product characteristics
package leaflet
carglumic acid
glutamates
drug approval
europe
administration, oral
carglumic acid
N-acetyl glutamate synthetase deficiency
amino-acid n-acetyltransferase
urea cycle disorders, inborn
propionic acidemia
Hyperammonemia due to N-acetylglutamate synthase deficiency
---
https://hpr-rps.hres.ca/reg-content/sommaire-motif-decision-detailTwo.php?lang=fr&linkID=SBD00176
2015
false
false
false
Canada
French
drug information
carglumic acid
carglumic acid
glutamates
---
http://www.has-sante.fr/portail/display.jsp?id=c_399846
http://www.has-sante.fr/portail/jcms/c_1720125/fr/carbaglu
2014
France
French
administration, oral
insurance, health, reimbursement
treatment outcome
carglumic acid
hyperammonemia
acidemia, isovaleric
methylmalonic acidemia
hyperammonemia
orphan drug production
amino acid metabolism, inborn errors
propionic acidemia
Isovaleryl-CoA dehydrogenase
glutamates
carglumic acid
evaluation of the transparency committee
---
https://www.ema.europa.eu/medicines/human/EPAR/Carbaglu
2011
United Kingdom
English
French
syndication feed
hyperammonemia
glutamates
treatment outcome
drug evaluation
carglumic acid
drug evaluation
summary of product characteristics
package leaflet
carglumic acid
glutamates
drug approval
europe
administration, oral
orphan drug production
carglumic acid
N-acetyl glutamate synthetase deficiency
acidemia, isovaleric
methylmalonic acidemia
urea cycle disorders, inborn
amino-acid n-acetyltransferase
amino acid metabolism, inborn errors
propionic acidemia
Isovaleryl-CoA dehydrogenase
Hyperammonemia due to N-acetylglutamate synthase deficiency
---
http://www.has-sante.fr/portail/upload/docs/application/pdf/ct031415.pdf
2003
France
French
hyperammonemia
infant, newborn
child
adult
orphan drug production
glutamates
carglumic acid
carglumic acid
evaluation of the transparency committee
---
http://www.has-sante.fr/portail/display.jsp?id=c_244608
2003
France
French
orphan drug production
glutamates
amino-acid n-acetyltransferase
hyperammonemia
carglumic acid
carglumic acid
guidelines for drug use
---