lymphohistiocytosis, hemophagocytic

Preferred Label : lymphohistiocytosis, hemophagocytic;

MeSH definition : A group of related disorders characterized by LYMPHOCYTOSIS; HISTIOCYTOSIS; and hemophagocytosis. The two major forms are familial and reactive.;

MeSH synonym : lymphohistiocytoses, hemophagocytic; hemophagocytic lymphohistiocytoses; hemophagocytic lymphohistiocytosis;

CISMeF synonym : hemophagocytic syndromes;

MeSH Hyperonym : Hemophagocytic Syndrome;

MeSH hyponym : familial hemophagocytic lymphocytosis; reactive hemophagocytic syndrome; Familial Hemophagocytic Lymphocytoses; Hemophagocytic Lymphocytoses, Familial; Hemophagocytic Lymphocytosis, Familial; Lymphocytoses, Familial Hemophagocytic; Lymphocytosis, Familial Hemophagocytic; Familial Erythrophagocytic Lymphohistiocytosis; Familial Histiocytic Reticulosis; Familial Histiocytic Reticuloses; Histiocytic Reticuloses, Familial; Histiocytic Reticulosis, Familial; Reticuloses, Familial Histiocytic; Hemophagocytic Lymphohistiocytosis Familial -1; Hemophagocytic Lymphohistiocytosis Familial 1; Hemophagocytic Lymphohistiocytosis, Familial; Familial Hemophagocytic Lymphohistiocytoses; Hemophagocytic Lymphohistiocytoses, Familial; Lymphohistiocytoses, Familial Hemophagocytic; Lymphohistiocytosis, Familial Hemophagocytic; Primary Hemophagocytic Hymphohistiocytosis; Hemophagocytic Hymphohistiocytoses, Primary; Hemophagocytic Hymphohistiocytosis, Primary; Hymphohistiocytoses, Primary Hemophagocytic; Hymphohistiocytosis, Primary Hemophagocytic; Primary Hemophagocytic Hymphohistiocytoses; Hemophagocytic Reticulosis, Familial; Familial Hemophagocytic Reticuloses; Hemophagocytic Reticuloses, Familial; Reticuloses, Familial Hemophagocytic; Reticulosis, Familial Hemophagocytic; Primary Hemophagocytic Lymphohistiocytosis; Hemophagocytic Lymphohistiocytoses, Primary; Hemophagocytic Lymphohistiocytosis, Primary; Lymphohistiocytoses, Primary Hemophagocytic; Lymphohistiocytosis, Primary Hemophagocytic; Primary Hemophagocytic Lymphohistiocytoses; Reticulosis, Familial Histiocytic; Familial Hemophagocytic Lymphohistiocytosis; Familial Hemophagocytic Histiocytosis; Familial Hemophagocytic Histiocytoses; Hemophagocytic Histiocytoses, Familial; Hemophagocytic Histiocytosis, Familial; Histiocytoses, Familial Hemophagocytic; Histiocytosis, Familial Hemophagocytic; Familial Hemophagocytic Reticulosis; Erythrophagocytic Lymphohistiocytosis, Familial; Erythrophagocytic Lymphohistiocytoses, Familial; Familial Erythrophagocytic Lymphohistiocytoses; Lymphohistiocytoses, Familial Erythrophagocytic; Lymphohistiocytosis, Familial Erythrophagocytic; Hemophagocytic Lymphohistiocytosis, Familial, 1; Hemophagocytic Syndrome, Reactive; Hemophagocytic Syndrome, Infection-Associated; Hemophagocytic Syndrome, Infection Associated; Infection-Associated Hemophagocytic Syndrome;

Wikipedia link : https://en.wikipedia.org/wiki/Hemophagocytic lymphohistiocytosis;

Details

Origin ID

D051359;

UMLS CUI

C0024291;

Allowable qualifiers
- blood [MeSH Qualifier]
- cerebrospinal fluid [MeSH Qualifier]
- chemically induced [MeSH Qualifier]
- classification [MeSH Qualifier]
- complications [MeSH Qualifier]
- congenital [MeSH Qualifier]
- diagnosis [MeSH Qualifier]
- diagnostic imaging [MeSH Qualifier]
- diet therapy [MeSH Qualifier]
- drug therapy [MeSH Qualifier]
- economics [MeSH Qualifier]
- embryology [MeSH Qualifier]
- enzymology [MeSH Qualifier]
- epidemiology [MeSH Qualifier]
- ethnology [MeSH Qualifier]
- etiology [MeSH Qualifier]
- genetics [MeSH Qualifier]
- history [MeSH Qualifier]
- immunology [MeSH Qualifier]
- metabolism [MeSH Qualifier]
- microbiology [MeSH Qualifier]
- mortality [MeSH Qualifier]
- nursing [MeSH Qualifier]
- parasitology [MeSH Qualifier]
- pathology [MeSH Qualifier]
- physiopathology [MeSH Qualifier]
- prevention and control [MeSH Qualifier]
- psychology [MeSH Qualifier]
- radiotherapy [MeSH Qualifier]
- rehabilitation [MeSH Qualifier]
- surgery [MeSH Qualifier]
- therapy [MeSH Qualifier]
- urine [MeSH Qualifier]
- veterinary [MeSH Qualifier]
- virology [MeSH Qualifier]
Automatic exact mappings (from CISMeF team)
- Haemophagocytic syndrome, infection-associated [ICD-10 Sub-category (who)]
- Hemophagocytic lymphohistiocytosis due to infection (disorder) [SNOMED CT concept]
- Hemophagocytic lymphohistiocytosis, familial [OMIM phenotypic series]
- Hemophagocytic syndrome associated with an infection [ORDO Disease]
- Reactive haemophagocytic syndrome [MedDRA LLT]
- Reactive hemophagocytic syndrome [MedDRA LLT]
- Secondary hemophagocytic lymphohistiocytosis [ORDO Disease]
Currated CISMeF NLP mapping
- Familial Hemophagocytic Lymphohistiocytosis [NCIt concept]
- Familial haemophagocytic lymphohistiocytosis [MedDRA Preferred Term]
- Familial hemophagocytic lymphohistiocytosis [ORDO Disease]
- Familial hemophagocytic lymphohistiocytosis [MedDRA LLT]
- Familial hemophagocytic lymphohistiocytosis (disorder) [SNOMED CT concept]
- Familial histiocytic reticulosis [PASCAL descriptor]
- Haemophagocytic lymphohistiocytosis [MedDRA LLT]
- Haemophagocytic lymphohistiocytosis [ICD-10 Sub-category (who)]
- Haemophagocytic lymphohistiocytosis [MedDRA Preferred Term]
- Haemophagocytic lymphohistiocytosis (disorder) [Inactive SNOMED CT concept]
- Haemophagocytic syndrome [MedDRA LLT]
- Hemophagocytic Lymphohistiocytosis [NCIt concept]
- Hemophagocytic Syndrome [NCIt concept]
- Hemophagocytic lymphohistiocytosis [PASCAL descriptor]
- Hemophagocytic lymphohistiocytosis [ICD-10 Sub-category]
- Hemophagocytic lymphohistiocytosis [MedDRA LLT]
- Hemophagocytic lymphohistiocytosis (disorder) [SNOMED CT concept]
- Hemophagocytic lymphohistiocytosis, familial, 1 [OMIM Phenotype]
- Hemophagocytic syndrome [PASCAL descriptor]
- Hemophagocytic syndrome [ORDO Disease]
- Hemophagocytic syndrome [MedDRA LLT]
- Hemophagocytic syndrome (disorder) [Inactive SNOMED CT concept]
- Hemophagocytic syndromes [ICD-9 code]
- Primary haemophagocytic lymphohistiocytosis [ICD-11 Sub-sub category]
- Primary hemophagocytic lymphohistiocytosis [MedDRA LLT]
- Primary hemophagocytic lymphohistiocytosis [ORDO Disease]
- familial hemophagocytic histiocytosis [SNOMED Notion]
- familial hemophagocytic lymphohistiocytosis 1 [DO Concept]
- haemophagocytic lymphohistiocytosis [COVID-19 Thesaurus concept]
- hemophagocytic lymphohistiocytosis [DO Concept]
- hemophagocytic lymphohistiocytosis [Disease (Nov.)]
- hemophagocytic lymphohistiocytosis [Radlex concept]
- non-Langerhans cell histiocytosis [Radlex concept]
DO Cross reference
- hemophagocytic lymphohistiocytosis [DO Concept]
Indexing information
- Emapalumab [MeSH Supplementary Concept]
Manual BTNT mappings - CISMeF
- Griscelli syndrome type 2 [ORDO Disease]
- Primary hemophagocytic lymphohistiocytosis [ORDO Disease]
- Secondary hemophagocytic lymphohistiocytosis [ORDO Disease]
Manual NTBT mappings (CISMeF)
- Immune dysregulation disease with immunodeficiency [ORDO Disease]
Record concept(s)
- Hemophagocytic Lymphohistiocytosis, Familial, 1 [MeSH concept]
- Hemophagocytic Syndromes [MeSH concept]
- familial hemophagocytic lymphocytosis [MeSH concept]
- lymphohistiocytosis, hemophagocytic [MeSH concept]
- reactive hemophagocytic syndrome [MeSH concept]
Related MeSH Supplementary Concept(s)
- griscelli syndrome type 2 [MeSH Supplementary Concept]
- hemophagocytic lymphohistiocytosis, familial, 2 [MeSH Supplementary Concept]
- hemophagocytic lymphohistiocytosis, familial, 3 [MeSH Supplementary Concept]
- hemophagocytic lymphohistiocytosis, familial, 4 [MeSH Supplementary Concept]
- hemophagocytic lymphohistiocytosis, familial, 5 [MeSH Supplementary Concept]
See also (suggested by CISMeF)
- macrophage activation syndrome [MeSH Descriptor]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Haemophagocytic lymphohistiocytosis [MedDRA LLT]
- Haemophagocytic lymphohistiocytosis [ICD-10 Sub-category (who)]
- Haemophagocytic lymphohistiocytosis [MedDRA Preferred Term]
- Hemophagocytic Lymphohistiocytosis [NCIt concept]
- Hemophagocytic lymphohistiocytosis [MedDRA LLT]
- Hemophagocytic lymphohistiocytosis [ICD-10 Sub-category]
- Hemophagocytic lymphohistiocytosis [PASCAL descriptor]
- Hemophagocytic lymphohistiocytosis (disorder) [SNOMED CT concept]
- Hemophagocytic syndrome [ORDO Disease]
- hemophagocytic lymphohistiocytosis [Radlex concept]
- hemophagocytic lymphohistiocytosis [DO Concept]
Validated automatic mappings to BTNT
- Familial haemophagocytic lymphohistiocytosis [ICD-11 More detail]

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