Definition : Group of disorders which feature accumulations of active histiocytes and lymphocytes,
but where the histiocytes are not langerhans cells. The group includes hemophagocytic
lymphohistiocytosis; sinus histiocytosis; xanthogranuloma; reticulohistiocytoma; juvenile
xanthogranuloma; xanthoma disseminatum; as well as the lipid storage diseases (sea-blue
histiocyte syndrome; and niemann-PICK DIseaSES). [MeSH];
Group of disorders which feature accumulations of active histiocytes and lymphocytes,
but where the histiocytes are not langerhans cells. The group includes hemophagocytic
lymphohistiocytosis; sinus histiocytosis; xanthogranuloma; reticulohistiocytoma; juvenile
xanthogranuloma; xanthoma disseminatum; as well as the lipid storage diseases (sea-blue
histiocyte syndrome; and niemann-PICK DIseaSES). [MeSH]