histiocytosis, Langerhans-Cell

Preferred Label : histiocytosis, Langerhans-Cell;

MeSH definition : A group of disorders resulting from the abnormal proliferation of and tissue infiltration by LANGERHANS CELLS which can be detected by their characteristic Birbeck granules (X bodies), or by monoclonal antibody staining for their surface CD1 ANTIGENS. Langerhans-cell granulomatosis can involve a single organ, or can be a systemic disorder.;

MeSH synonym : disease, schueller-christian; schueller christian disease; generalized histiocytoses; histiocytosis x; histiocytosis, generalized; granulomatosis, langerhans-cell; schueller-christian disease; histiocytosis-x; langerhans-cell histiocytosis; langerhans cell histiocytosis; langerhans-cell granulomatosis; langerhans cell granulomatosis; generalized histiocytosis; histiocytoses, generalized; Non-Lipid reticuloendotheliosis; non lipid reticuloendotheliosis; Non-Lipid reticuloendothelioses; reticuloendothelioses, Non-Lipid; reticuloendotheliosis, Non-Lipid; systemic aleukemic reticuloendotheliosis; aleukemic reticuloendothelioses, systemic; aleukemic reticuloendotheliosis, systemic; reticuloendothelioses, systemic aleukemic; reticuloendotheliosis, systemic aleukemic; systemic aleukemic reticuloendothelioses; type 2 histiocytosis; histiocytoses, type 2; histiocytosis, type 2; type 2 histiocytoses; histiocytosis, langerhans cell; cell histiocytoses, langerhans; cell histiocytosis, langerhans; histiocytoses, langerhans cell; langerhans cell histiocytoses; cell granulomatoses, langerhans; cell granulomatosis, langerhans; granulomatoses, langerhans cell; granulomatosis, langerhans cell; langerhans cell granulomatoses;

CISMeF synonym : letterer-siwe disease; hand-schueller-christian syndrome;

DeCS synonym : Hand-Sch ller-Christian Disease; Hand Sch ller Christian Syndrome; Hand Sch ller Christian Disease; Hand-Sch ller-Christian Syndrome;

MeSH Hyperonym : Hand Schueller Christian Syndrome; Syndrome, Hand-Schueller-Christian; Hand-Schüller-Christian Syndrome; Hand Schüller Christian Syndrome; Syndrome, Hand-Schüller-Christian; Hand-Schüller-Christian Disease; Disease, Hand-Schüller-Christian; Hand Schüller Christian Disease; Hand-Schueller-Christian Disease; Disease, Hand-Schueller-Christian; Hand Schueller Christian Disease;

MeSH hyponym : pulmonary histiocytosis X; Hashimoto-Pritzger disease; Histiocytosis X, Pulmonary; Pulmonary Langerhans Cell Granulomatosis; Langerhans Cell Granulomatosis, Pulmonary; Disease, Hashimoto-Pritzger; Diseases, Hashimoto-Pritzger; Hashimoto Pritzger Disease; Hashimoto-Pritzger Diseases; Disease, Letterer-Siwe; Letterer Siwe Disease;

Wikipedia link : https://en.wikipedia.org/wiki/Langerhans cell histiocytosis;

Details

Origin ID

D006646;

UMLS CUI

C0019621;

Allowable qualifiers
- blood [MeSH Qualifier]
- cerebrospinal fluid [MeSH Qualifier]
- chemically induced [MeSH Qualifier]
- classification [MeSH Qualifier]
- complications [MeSH Qualifier]
- congenital [MeSH Qualifier]
- diagnosis [MeSH Qualifier]
- diagnostic imaging [MeSH Qualifier]
- diet therapy [MeSH Qualifier]
- drug therapy [MeSH Qualifier]
- economics [MeSH Qualifier]
- embryology [MeSH Qualifier]
- enzymology [MeSH Qualifier]
- epidemiology [MeSH Qualifier]
- ethnology [MeSH Qualifier]
- etiology [MeSH Qualifier]
- genetics [MeSH Qualifier]
- history [MeSH Qualifier]
- immunology [MeSH Qualifier]
- metabolism [MeSH Qualifier]
- microbiology [MeSH Qualifier]
- mortality [MeSH Qualifier]
- nursing [MeSH Qualifier]
- parasitology [MeSH Qualifier]
- pathology [MeSH Qualifier]
- physiopathology [MeSH Qualifier]
- prevention and control [MeSH Qualifier]
- psychology [MeSH Qualifier]
- radiotherapy [MeSH Qualifier]
- rehabilitation [MeSH Qualifier]
- surgery [MeSH Qualifier]
- therapy [MeSH Qualifier]
- urine [MeSH Qualifier]
- veterinary [MeSH Qualifier]
- virology [MeSH Qualifier]
Automatic exact mappings (from CISMeF team)
- Adult Langerhans Cell Histiocytosis [NCIt concept]
- Adult pulmonary Langerhans cell histiocytosis [ORDO Disease]
- Childhood Langerhans Cell Histiocytosis [NCIt concept]
- HISTIOCYTOSIS [ACR pathology]
- HISTIOCYTOSIS [ACR pathology]
- Hand Schuller Christian disease [PASCAL descriptor]
- Hand-Schueller-Christian disease [MedDRA LLT]
- Hand-Schuller-Christian Disease [NCIt concept]
- Hand-Schuller-Christian disease [ICD-11 Extension code]
- Hand-Schuller-Christian disease [ACR pathology]
- Hand-Schuller-Christian disease [ACR pathology]
- Hand-Schuller-Christian disease [ACR pathology]
- Hand-Schuller-Christian disease [Radlex concept]
- Hand-Schüller-Christian disease [ICD-11 More detail]
- Hand-Schüller-Christian disease [ORDO Disease]
- Hand-Schüller-Christian disease (disorder) [SNOMED CT concept]
- Histiocytosis [PASCAL descriptor]
- Histiocytosis [NCIt concept]
- Histiocytosis [MedDRA Preferred Term]
- Histiocytosis (morphologic abnormality) [SNOMED CT concept]
- Histiocytosis X of lung [MedDRA LLT]
- Histiocytosis X syndrome (disorder) [SNOMED CT concept]
- Langerhans cell histiocytosis [ICD-11 Subcategory]
- Langerhans cell histiocytosis [ICD-11 Extension code]
- Langerhans cell histiocytosis, disseminated (disorder) [SNOMED CT concept]
- Langerhans cell histiocytosis, disseminated (morphologic abnormality) [SNOMED CT concept]
- Letterer Siwe disease [PASCAL descriptor]
- Letterer-Siwe Disease [NCIt concept]
- Letterer-Siwe disease [ICD-11 Extension code]
- Letterer-Siwe disease [ICD-11 Extension code]
- Letterer-Siwe disease [ICD-10 Sub-category (who)]
- Letterer-Siwe disease [ICD-9 code]
- Letterer-Siwe disease [ACR pathology]
- Letterer-Siwe disease [ACR pathology]
- Letterer-Siwe disease [ACR pathology]
- Letterer-Siwe disease [Radlex concept]
- Letterer-Siwe disease [ORDO Disease]
- Letterer-Siwe disease [MedDRA LLT]
- Letterer-Siwe's disease [ICD-9 code]
- Letterer-siwe disease [OMIM Phenotype]
- Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis [ICD-10 Sub-category]
- Multifocal and unisystemic Langerhans-cell histiocytosis [ICD-10 Sub-category]
- Non langerhans cell histiocytosis [PASCAL descriptor]
- Nonlipid reticuloendotheliosis [ICD-11 Extension code]
- Pulmonary eosinophilic granuloma [PASCAL descriptor]
- granuloma, nos [SNOMED Notion]
- hand-schuller-christian disease [SNOMED Notion]
- histiocytosis [Radlex concept]
- histiocytosis [DO Concept]
- histiocytosis, nos [SNOMED Notion]
Currated CISMeF NLP mapping
- Langerhans Cell Histiocytosis [NCIt concept]
- Langerhans cell histiocytosis [PASCAL descriptor]
- Langerhans cell histiocytosis [OMIM Phenotype]
- Langerhans cell histiocytosis [Radlex concept]
- Langerhans cell histiocytosis [ORDO Disease]
- Langerhans cell histiocytosis (disorder) [SNOMED CT concept]
- Langerhans cell histiocytosis, NOS [ICD-O code]
- Langerhans cell histiocytosis, no International Classification of Diseases for Oncology subtype (morphologic abnormality) [Inactive SNOMED CT concept]
- Langerhans cell histiocytosis, not elsewhere classified [ICD-10 Sub-category (who)]
- Langerhans' cell granulomatosis [MedDRA LLT]
- Langerhans' cell histiocytosis [MedDRA Preferred Term]
- Langerhans-cell histiocytosis [DO Concept]
- langerhans cell histiocytosis [Disease (Nov.)]
DO Cross reference
- Langerhans-cell histiocytosis [DO Concept]
Manual BTNT mappings - CISMeF
- Adult pulmonary Langerhans cell histiocytosis [ORDO Disease]
- Hashimoto-Pritzker syndrome [ORDO Disease]
Manual NTBT mappings (CISMeF)
- Dendritic cell tumor [ORDO Disease]
- Pituitary hormone deficiency secondary to a granulomatous disease [ORDO Disease]
Ne pas confondre avec
- histiocytosis [MeSH Descriptor]
ORDO relation(s)
- Langerhans cell histiocytosis [ORDO Disease]
Record concept(s)
- Hand-Schueller-Christian Syndrome [MeSH concept]
- Hashimoto-Pritzger disease [MeSH concept]
- Letterer-Siwe Disease [MeSH concept]
- histiocytosis, Langerhans-Cell [MeSH concept]
- pulmonary histiocytosis X [MeSH concept]
Related MeSH Supplementary Concept(s)
- Hashimoto-Pritzker syndrome [MeSH Supplementary Concept]
- familial Letterer-Siwe disease [MeSH Supplementary Concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Chronic idiopathic xanthomatosis [MedDRA LLT]
- Hand Schuller Christian disease [PASCAL descriptor]
- Hand-Schueller-Christian disease [MedDRA LLT]
- Hand-Schuller-Christian Disease [NCIt concept]
- Hand-Schuller-Christian disease [Radlex concept]
- Hand-Schüller-Christian disease [ORDO Disease]
- Hand-Schüller-Christian disease (disorder) [SNOMED CT concept]
- Histiocytosis X syndrome (disorder) [SNOMED CT concept]
- Langerhans Cell Histiocytosis [NCIt concept]
- Langerhans cell histiocytosis [ORDO Disease]
- Langerhans cell histiocytosis [OMIM Phenotype]
- Langerhans cell histiocytosis [Radlex concept]
- Langerhans cell histiocytosis [PASCAL descriptor]
- Langerhans cell histiocytosis (disorder) [SNOMED CT concept]
- Langerhans cell histiocytosis, NOS [ICD-O code]
- Langerhans cell histiocytosis, multifocal (morphologic abnormality) [SNOMED CT concept]
- Langerhans cell histiocytosis, no International Classification of Diseases for Oncology subtype (morphologic abnormality) [Inactive SNOMED CT concept]
- Langerhans' cell granulomatosis [MedDRA LLT]
- Langerhans' cell histiocytosis [MedDRA Preferred Term]
- Langerhans' cell histiocytosis (morphologic abnormality) [SNOMED CT concept]
- Langerhans-cell histiocytosis [DO Concept]
- hand-schuller-christian disease [SNOMED Notion]
- langerhans cell histiocytosis [Disease (Nov.)]
Validated automatic mappings to BTNT
- Pulmonary Langerhans Cell Histiocytosis [NCIt concept]

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