Langerhans cell histiocytosis

Preferred Label : Langerhans cell histiocytosis;

RADLEX synonyms : histiocytosis X;

Definition : Group of disorders characterized by monoclonal proliferation of CD1 histiocytes. The demonstration of the langerhans cells birbeck granules is the gold standard of the phenotype. eosinophilic granuloma makes up 60-80% of all the cases. [MeSH];

UMLS CUI (RADLEX) : C0019621;

Details

Origin ID

RID3846;

UMLS CUI

C0019621;

Associated condition of
- floating tooth sign [Radlex concept]
- hole-within-a-hole pattern [Radlex concept]
Automatic exact mappings (from CISMeF team)
- Adult Langerhans Cell Histiocytosis [NCIt concept]
- Childhood Langerhans Cell Histiocytosis [NCIt concept]
- Langerhans cell histiocytosis [ICD-11 Subcategory]
- Non langerhans cell histiocytosis [PASCAL descriptor]
- histiocytosis, non-langerhans-cell [MeSH Descriptor]
Currated CISMeF NLP mapping
- Langerhans Cell Histiocytosis [NCIt concept]
- Langerhans cell histiocytosis [PASCAL descriptor]
- Langerhans cell histiocytosis [OMIM Phenotype]
- Langerhans cell histiocytosis [ORDO Disease]
- Langerhans cell histiocytosis (disorder) [SNOMED CT concept]
- Langerhans cell histiocytosis, NOS [ICD-O code]
- Langerhans cell histiocytosis, no International Classification of Diseases for Oncology subtype (morphologic abnormality) [Inactive SNOMED CT concept]
- Langerhans' cell histiocytosis [MedDRA Preferred Term]
- Langerhans-cell histiocytosis [DO Concept]
- histiocytosis, Langerhans-Cell [MeSH Descriptor]
- histiocytosis, Langerhans-Cell [MeSH concept]
- langerhans cell histiocytosis [Disease (Nov.)]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Chronic idiopathic xanthomatosis [MedDRA LLT]
- Hand Schuller Christian disease [PASCAL descriptor]
- Hand-Schueller-Christian disease [MedDRA LLT]
- Hand-Schuller-Christian Disease [NCIt concept]
- Hand-Schüller-Christian disease [ORDO Disease]
- Hand-Schüller-Christian disease (disorder) [SNOMED CT concept]
- Histiocytosis X syndrome (disorder) [SNOMED CT concept]
- Langerhans Cell Histiocytosis [NCIt concept]
- Langerhans cell histiocytosis [OMIM Phenotype]
- Langerhans cell histiocytosis [ORDO Disease]
- Langerhans cell histiocytosis [PASCAL descriptor]
- Langerhans cell histiocytosis (disorder) [SNOMED CT concept]
- Langerhans cell histiocytosis, NOS [ICD-O code]
- Langerhans cell histiocytosis, multifocal (morphologic abnormality) [SNOMED CT concept]
- Langerhans cell histiocytosis, no International Classification of Diseases for Oncology subtype (morphologic abnormality) [Inactive SNOMED CT concept]
- Langerhans' cell granulomatosis [MedDRA LLT]
- Langerhans' cell histiocytosis [MedDRA Preferred Term]
- Langerhans' cell histiocytosis (morphologic abnormality) [SNOMED CT concept]
- Langerhans-cell histiocytosis [DO Concept]
- hand-schuller-christian disease [SNOMED Notion]
- histiocytosis, Langerhans-Cell [MeSH Descriptor]
- histiocytosis, Langerhans-Cell [MeSH concept]
- langerhans cell histiocytosis [Disease (Nov.)]

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