Primary pulmonary hypertension

Preferred Label : Primary pulmonary hypertension;

Inclusion CIM-10 : Primary group 1 pulmonary hypertension; Heritable pulmonary arterial hypertension; Idiopathic pulmonary arterial hypertension; Primary pulmonary arterial hypertension;

ICD-10 exclusion note : pulmonary hypertension NOS (I27.20); secondary pulmonary hypertension (I27.29); secondary pulmonary arterial hypertension (I27.21); persistent pulmonary hypertension of newborn (P29.30);

Diag associé à un acte (%) : 90.0;

CMA : 2;

Source : OMS;

Date de début : 01/01/1997;

Details

Origin ID

I270;

UMLS CUI

C0152171;

Automatic exact mappings (from CISMeF team)
- Cor pulmonale [HPO term]
- Elbow hypertrichosis [HPO term]
- Familial Primary Pulmonary Hypertension [MeSH Descriptor]
- Familial primary pulmonary hypertension (disorder) [SNOMED CT concept]
- Familial pulmonary arterial hypertension [ICD-11 More detail]
- Hereditary pyropoikilocytosis (disorder) [SNOMED CT concept]
- Heritable Pulmonary Arterial Hypertension [NCIt concept]
- Heritable pulmonary arterial hypertension (disorder) [SNOMED CT concept]
- Hypophosphatasia [ORDO Disease]
- Idiopathic pulmonary arterial hypertension [ICD-11 More detail]
- Primary Pulmonary Hypertension [NCIt concept]
- Primary pulmonary hypertension (disorder) [Inactive SNOMED CT concept]
- Pulmonary arterial hypertension [HPO term]
- Pulmonary arterial hypertension [ICD-11 Subcategory]
- Pulmonary hypertension, primary (see also hereditary hemorrhagic telangiectasia ({ps187300}) [OMIM phenotypic series]
- Pyropoikilocytosis, hereditary [OMIM Phenotype]
- allopurinol [MeSH Descriptor]
- familial hyperkalemic periodic paralysis [SNOMED Notion]
- paralysis, hyperkalemic periodic [MeSH Descriptor]
- paralysis, hyperkalemic periodic [MeSH concept]
- postpartum hemorrhage [MeSH Descriptor]
- pulmonary hypertension [MedlinePlus Topic]
Currated CISMeF NLP mapping
- Idiopathic Pulmonary Hypertension [NCIt concept]
- Idiopathic pulmonary arterial hypertension [ORDO Disease]
- Idiopathic pulmonary arterial hypertension [MedDRA LLT]
- Idiopathic pulmonary arterial hypertension (disorder) [SNOMED CT concept]
- Primary pulmonary hypertension [MedDRA LLT]
- Primary pulmonary hypertension [ICD-9 code]
- Primary pulmonary hypertension [ICD-10 Sub-category (who)]
- Pulmonary hypertension primary [MedDRA LLT]
- primary pulmonary hypertension [SNOMED Notion]
- primary pulmonary hypertension [Disease (Nov.)]
- primary pulmonary hypertension [DO Concept]
DO Cross reference
- primary pulmonary hypertension [DO Concept]
Orphanet concepts
- Heritable pulmonary arterial hypertension [ORDO Disease]
- Idiopathic pulmonary arterial hypertension [ORDO Disease]
- Idiopathic/heritable pulmonary arterial hypertension [ORDO Disease]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Idiopathic Pulmonary Hypertension [NCIt concept]
- Primary pulmonary hypertension [MedDRA LLT]
- Primary pulmonary hypertension [ICD-9 code]
- Primary pulmonary hypertension (disorder) [Inactive SNOMED CT concept]
- Pulmonary hypertension primary [MedDRA LLT]
- primary pulmonary hypertension [SNOMED Notion]
- primary pulmonary hypertension [DO Concept]
- primary pulmonary hypertension [Disease (Nov.)]
Validated automatic mappings to BTNT
- Heritable pulmonary arterial hypertension [ORDO Disease]

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