Pulmonary arterial hypertension

ICD-11 code : BB01.0;

Preferred Label : Pulmonary arterial hypertension;

ICD-11 definition : Pulmonary arterial hypertension is a clinical condition characterized by the presence of pre-capillary pulmonary hypertension in the absence of other causes of pre-capillary pulmonary hypertension, such as due to lung diseases, chronic thromboembolic pulmonary hypertension, or other rare diseases. It includes different forms that share a similar clinical picture and virtually identical pathological changes of the lung microcirculation.;

ICD-11 synonym : Arrillaga Ayerza syndrome; PAH - [pulmonary arterial hypertension]; primary pulmonary hypertension;

ICD-11 acronym : PAH;

ICD-11 inclusion : primary pulmonary hypertension;

Details

Origin ID

1931148955;

Automatic exact mappings (from CISMeF team)
- Familial Primary Pulmonary Hypertension [MeSH Descriptor]
- Phenylalanine hydroxylase [OMIM gene]
- Primary Pulmonary Hypertension [NCIt concept]
- Primary pulmonary hypertension [MedDRA LLT]
- Primary pulmonary hypertension [ICD-9 code]
- Primary pulmonary hypertension [ICD-10 Sub-category]
- Pulmonary artery hypoplasia [ORDO Disease]
- Pulmonary hypertension primary [MedDRA LLT]
- Pulmonary hypertension, primary (see also hereditary hemorrhagic telangiectasia ({ps187300}) [OMIM phenotypic series]
- phenylalanine hydroxylase [ORDO Gene]
- primary pulmonary hypertension [DO Concept]
- primary pulmonary hypertension [SNOMED Notion]
- proclavaminate amidinohydrolase activity [GO term]
Currated CISMeF NLP mapping
- Pulmonary Arterial Hypertension [NCIt concept]
- Pulmonary Arterial Hypertension [MeSH Descriptor]
- Pulmonary arterial hypertension [HPO term]
- Pulmonary arterial hypertension [MedDRA Preferred Term]
- Pulmonary arterial hypertension [ORDO Disease]
- Pulmonary hypertension [HRDO Sign]
- Pulmonary hypertension [PASCAL descriptor]
- Pulmonary hypertension, primary, 1 [OMIM Phenotype]
- Pulmonary hypertensive arterial disease (disorder) [SNOMED CT concept]
- hypertension, pulmonary [MeSH Descriptor]
- hypertension, pulmonary [MeSH concept]
- pulmonary hypertension [MedlinePlus Topic]
False automatic mappings
- Para-Aminohippurate Sodium Measurement [NCIt concept]

Keyword's position in hierarchy(ies) :

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