Preferred Label : Familial pulmonary arterial hypertension;
ICD-11 definition : This is a familial increase of blood pressure in the pulmonary artery, pulmonary vein,
or pulmonary capillaries, together known as the lung vasculature, leading to shortness
of breath, dizziness, fainting, and other symptoms, all of which are exacerbated by
exertion.;
ICD-11 synonym : heritable pulmonary arterial hypertension;
ICD-11 inclusion : heritable pulmonary arterial hypertension;
Origin ID : 943760810;
UMLS CUI : C0340543;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
Semantic type(s)
UMLS correspondences (same concept)
This is a familial increase of blood pressure in the pulmonary artery, pulmonary vein,
or pulmonary capillaries, together known as the lung vasculature, leading to shortness
of breath, dizziness, fainting, and other symptoms, all of which are exacerbated by
exertion.