Preferred Label : linear IgA bullous dermatosis;
MeSH definition : Autoimmune disease characterized by subepidermal blisters and linear deposition of
autoantibodies at the dermoepidermal junction. The accumulated autoantibodies are
of IMMUNOGLOBULIN A and occasionally IMMUNOGLOBULIN G classes against epidermal BASEMENT
MEMBRANE proteins. The dermatosis is sometimes associated with malignancies and use
of certain drugs (e.g., VANCOMYCIN).;
MeSH synonym : linear IgA dermatosis; dermatoses, linear IgA; dermatosis, linear IgA; IgA dermatoses, linear; IgA dermatosis, linear; linear IgA dermatoses;
CISMeF synonym : IgA/IgG dermatoses, linear; IgA/IgG dermatosis, linear; dermatoses, linear IgA/IgG; dermatosis, linear IgA/IgG; linear IgA/IgG bullous dermatosis; linear IgA/IgG dermatoses; linear IgA/IgG dermatosis;
MeSH hyponym : chronic bullous disease of childhood; drug-induced linear IgA bullous dermatosis; Drug induced Linear IgA Bullous Dermatosis; Drug-induced Linear IgA Dermatosis; Drug induced Linear IgA Dermatosis;
Related MeSH term : linear IgA IgG bullous dermatosis; Linear IgA IgG Dermatosis;
Wikipedia link : https://en.wikipedia.org/wiki/Chronic bullous disease of childhood;
Origin ID : D062027;
UMLS CUI : C0406650;
Allowable qualifiers
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
Record concept(s)
Semantic type(s)
UMLS correspondences (same concept)
Autoimmune disease characterized by subepidermal blisters and linear deposition of
autoantibodies at the dermoepidermal junction. The accumulated autoantibodies are
of IMMUNOGLOBULIN A and occasionally IMMUNOGLOBULIN G classes against epidermal BASEMENT
MEMBRANE proteins. The dermatosis is sometimes associated with malignancies and use
of certain drugs (e.g., VANCOMYCIN).
https://www.medg.fr/dermatoses-a-iga-lineaire
2021
France
teaching material
scientific and technical information
Linear dermatosis
linear IgA bullous dermatosis
linear iga dermatosis
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http://www.has-sante.fr/portail/jcms/c_2636268/fr/maladies-bulleuses-auto-immunes-dermatose-a-iga-lineaire
http://www.has-sante.fr/portail/jcms/c_2636267/fr/pnds-dermatose-a-iga-lineaire
2016
false
false
false
France
French
practice guideline
linear IgA bullous dermatosis
linear IgA bullous dermatosis
linear IgA bullous dermatosis
general practice
watchful waiting
general practitioners
---
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=46488
false
true
false
France
scientific and technical information
linear IgA bullous dermatosis
linear iga dermatosis
---
http://www.dermis.net/dermisroot/fr/30140/diagnose.htm
false
true
false
Germany
image
scientific and technical information
linear iga dermatosis
linear IgA bullous dermatosis
---