Preferred Label : linear IgA bullous dermatosis;
MeSH definition : Autoimmune disease characterized by subepidermal blisters and linear deposition of
autoantibodies at the dermoepidermal junction. The accumulated autoantibodies are
of IMMUNOGLOBULIN A and occasionally IMMUNOGLOBULIN G classes against epidermal BASEMENT
MEMBRANE proteins. The dermatosis is sometimes associated with malignancies and use
of certain drugs (e.g., VANCOMYCIN).;
MeSH synonym : linear IgA dermatosis; dermatoses, linear IgA; dermatosis, linear IgA; IgA dermatoses, linear; IgA dermatosis, linear; linear IgA dermatoses;
CISMeF synonym : IgA/IgG dermatoses, linear; IgA/IgG dermatosis, linear; dermatoses, linear IgA/IgG; dermatosis, linear IgA/IgG; linear IgA/IgG bullous dermatosis; linear IgA/IgG dermatoses; linear IgA/IgG dermatosis;
MeSH hyponym : chronic bullous disease of childhood; drug-induced linear IgA bullous dermatosis; Drug induced Linear IgA Bullous Dermatosis; Drug-induced Linear IgA Dermatosis; Drug induced Linear IgA Dermatosis;
Related MeSH term : linear IgA IgG bullous dermatosis; Linear IgA IgG Dermatosis;
Wikipedia link : https://en.wikipedia.org/wiki/Chronic bullous disease of childhood;
Origin ID : D062027;
UMLS CUI : C0406650;
- Allowable qualifiers
- Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- Record concept(s)
- Semantic type(s)
- UMLS correspondences (same concept)
Autoimmune disease characterized by subepidermal blisters and linear deposition of
autoantibodies at the dermoepidermal junction. The accumulated autoantibodies are
of IMMUNOGLOBULIN A and occasionally IMMUNOGLOBULIN G classes against epidermal BASEMENT
MEMBRANE proteins. The dermatosis is sometimes associated with malignancies and use
of certain drugs (e.g., VANCOMYCIN).
https://www.medg.fr/dermatoses-a-iga-lineaire
2021
France
teaching material
scientific and technical information
Linear dermatosis
linear IgA bullous dermatosis
linear iga dermatosis
---
http://www.has-sante.fr/portail/jcms/c_2636268/fr/maladies-bulleuses-auto-immunes-dermatose-a-iga-lineaire
http://www.has-sante.fr/portail/jcms/c_2636267/fr/pnds-dermatose-a-iga-lineaire
2016
false
false
false
France
French
practice guideline
linear IgA bullous dermatosis
linear IgA bullous dermatosis
linear IgA bullous dermatosis
general practice
watchful waiting
general practitioners
---
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=46488
false
true
false
France
scientific and technical information
linear IgA bullous dermatosis
linear iga dermatosis
---
http://www.dermis.net/dermisroot/fr/30140/diagnose.htm
false
true
false
Germany
image
scientific and technical information
linear iga dermatosis
linear IgA bullous dermatosis
---