ICD-11 code : EB42;
Preferred Label : Linear IgA bullous dermatosis;
ICD-11 definition : Linear IgA bullous dermatosis is an uncommon immunobullous disorder which occurs in
both adults and children. It is characterized by linear deposition of IgA along the
epidermal basement membrane. Although the clinical picture may resemble dermatitis
herpetiformis, it is not associated with gluten enteropathy and it has different clinical
and immunopathological attributes.;
ICD-11 synonym : Linear IgA disease;
Origin ID : 1802341051;
Automatic exact mappings (from CISMeF team)
- ICD-10 Mapping
Linear IgA bullous dermatosis is an uncommon immunobullous disorder which occurs in
both adults and children. It is characterized by linear deposition of IgA along the
epidermal basement membrane. Although the clinical picture may resemble dermatitis
herpetiformis, it is not associated with gluten enteropathy and it has different clinical
and immunopathological attributes.
