Skin Undifferentiated Pleomorphic Sarcoma

Preferred Label : Skin Undifferentiated Pleomorphic Sarcoma;

NCIt synonyms : Malignant Skin Fibrous Histiocytoma; Malignant Fibrous Histiocytoma of Skin; Malignant Fibrous Histiocytoma of the Skin; Cutaneous Unclassified Pleomorphic Sarcoma (Formerly Cutaneous MFH); Cutaneous Unclassified Pleomorphic Sarcoma; Cutaneous Unclassified Pleomorphic Sarcoma (Formerly Cutaneous Malignant Fibrous Histiocytoma); Malignant Cutaneous Fibrous Histiocytoma; Cutaneous Malignant Fibrous Histiocytoma; PDS; Cutaneous Undifferentiated Pleomorphic Sarcoma; Pleomorphic Dermal Sarcoma;

NCIt definition : An undifferentiated pleomorphic sarcoma arising from the skin. It is characterized by the presence of spindle cells in a storiform pattern and histiocytes with abundant cytoplasm.;

Neoplastic status : Malignant;

Details

Origin ID

C5576;

UMLS CUI

C1275254;

Automatic exact mappings (from CISMeF team)
- After-Hours care [MeSH Descriptor]
- Ocular pigment dispersion with or without glaucoma [OMIM Phenotype]
- Pendred syndrome [OMIM Phenotype]
- Pleomorphic dermal sarcoma [ICD-11 Extension code]
- Prostaglandin d2 synthase, brain [OMIM gene]
- Unclassified pleomorphic sarcoma of skin [ICD-11 Subcategory]
- malignant skin fibrous histiocytoma [DO Concept]
- solute carrier family 26 member 4 [ORDO Gene]
CISMeF manual mappings
- Malignant fibrous histiocytoma of skin (disorder) [SNOMED CT concept]
DO Cross reference
- malignant skin fibrous histiocytoma [DO Concept]
Disease excludes normal cell origin
- Epithelial Cell [NCIt concept]
Excludes anatomical site(s)
- Bone [NCIt concept]
Has associated anatomic sites
- Connective and Soft Tissue [NCIt concept]
- Integumentary System [NCIt concept]
- Skin [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Malignant fibrous histiocytoma of skin (disorder) [SNOMED CT concept]
- malignant skin fibrous histiocytoma [DO Concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
- Favorable Clinical Outcome [NCIt concept]
- Indolent Clinical Course [NCIt concept]
- Intermediate Filaments Present [NCIt concept]
- Intracytoplasmic Eosinophilic Inclusion [NCIt concept]
disease_excludes_normal_tissue_origin
- Epithelial Tissue [NCIt concept]
disease_has_abnormal_cell
- Giant Cell [NCIt concept]
- Malignant Cell [NCIt concept]
- Malignant Spindle-Shaped Fibrohistiocytic Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Primitive Mesenchymal Cell [NCIt concept]
disease_has_finding
- Cellular Pleomorphism [NCIt concept]
- Cutaneous Involvement [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
- No Identifiable Line of Differentiation [NCIt concept]
- Storiform Growth Pattern [NCIt concept]
disease_has_normal_tissue_origin
- Connective and Soft Tissue [NCIt concept]
- Soft Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Dermis [NCIt concept]
- Skin [NCIt concept]
disease_may_have_cytogenetic_abnormality
- Double Minutes [NCIt concept]
- Gain of Chromosome 19 [NCIt concept]
- Gain of Chromosome 1p31 [NCIt concept]
- Gain of Chromosome 7p [NCIt concept]
- Gain of Chromosome 7q32 [NCIt concept]
- Loss of Chromosome 11 [NCIt concept]
- Loss of Chromosome 13 [NCIt concept]
- Loss of Chromosome 16 [NCIt concept]
- Loss of Chromosome 2p [NCIt concept]
- Loss of Chromosome 2q [NCIt concept]
- Supernumerary Circular Chromosome [NCIt concept]

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