Nasal Type Extranodal NK/T-Cell Lymphoma

Preferred Label : Nasal Type Extranodal NK/T-Cell Lymphoma;

NCIt synonyms : Angiocentric T-Cell Lymphoma; Nasal Type Extranodal NK T-Cell Lymphoma; Extranodal NK/T-Cell Lymphoma;

NCIt related terms : Extranodal NK/T lymphoma-nasal; RETICULOSIS, MALIGNANT; Extranodal NK/T-cell lymphoma, nasal type; NK/T-cell lymphoma, nasal and nasal-type; T/NK-cell lymphoma;

NCIt definition : An aggressive, predominantly extranodal, mature T-cell non-Hodgkin lymphoma. It is characterized by an often angiocentric and angiodestructive cellular infiltrate composed of EBV positive NK/T cells. The nasal cavity is the most common site of involvement. Patients often present with midfacial destructive lesions (lethal midline granuloma). The disease may disseminate rapidly to various anatomic sites including the gastrointestinal tract, skin, testis, and cervical lymph nodes. It is also known as angiocentric T-cell lymphoma. The term polymorphic reticulosis has been widely used to describe the morphologic changes seen in this type of lymphoma. However, the latter term may also apply to lymphomatoid granulomatosis, which is an angiocentric and angiodestructive EBV positive B-cell lymphoproliferative disorder.;

Alternative definition : CDISC: A malignant lymphoid neoplasm composed of EBV-positive NK/T cells arranged in an angiocentric pattern.;

Neoplastic status : Malignant;

ICD-O code : 9719/3;

Codes from synonyms : 10065855; C86.0;

Details

Origin ID

C4684;

UMLS CUI

C0392788;

Automatic exact mappings (from CISMeF team)
- Extranodal NK/T-cell lymphoma, nasal type [MedDRA LLT]
- Extranodal NK/T-cell lymphoma, nasal type [ICD-10 Sub-category]
- Malignant histiocytosis (disorder) [SNOMED CT concept]
- NK/T-cell lymphoma, nasal and nasal-type [ICD-11 More detail]
- Natural killer-/T-cell lymphoma, nasal and nasal-type (morphologic abnormality) [SNOMED CT concept]
- malignant histiocytosis [DO Concept]
- nasal type extranodal NK/T-cell lymphoma [DO Concept]
Currated CISMeF NLP mapping
- Extranodal NK/T-cell lymphoma, nasal type [ICD-11 Subcategory]
- Extranodal nasal NK/T cell lymphoma [ORDO Disease]
- Extranodal natural killer/T-cell lymphoma, nasal type (disorder) [SNOMED CT concept]
- NK/T-cell lymphoma, nasal and nasal-type [ICD-O code]
- extranodal NK-T-Cell lymphoma, nasal and Nasal-Type [MeSH concept]
- lymphoma, extranodal nk-t-cell [MeSH Descriptor]
DO Cross reference
- nasal type extranodal NK/T-cell lymphoma [DO Concept]
Disease excludes abnormal cell
- Lymphocyte Predominant Cell [NCIt concept]
- Neoplastic B-Lymphocyte [NCIt concept]
- Reed-Sternberg Cell [NCIt concept]
Disease excludes normal cell origin
- Myeloid Cell [NCIt concept]
- Plasma Cell [NCIt concept]
- Precursor Natural Killer Cell [NCIt concept]
- Precursor T-Lymphoblast [NCIt concept]
Disease may have findings
- Aggressive Clinical Course [NCIt concept]
- Coagulative Necrosis [NCIt concept]
- Diffuse Pattern [NCIt concept]
- Fever [NCIt concept]
- Hemophagocytosis [NCIt concept]
- High Mitotic Activity [NCIt concept]
- Lymphadenopathy [NCIt concept]
- Malaise [NCIt concept]
- Polymorphic Cellular Infiltrate [NCIt concept]
- Weight Loss [NCIt concept]
Excludes anatomical site(s)
- Lymph Node [NCIt concept]
Has associated anatomic sites
- Hematopoietic and Lymphatic System [NCIt concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Angiocentric lymphoma [MedDRA Preferred Term]
- Angiocentric lymphoma NOS [MedDRA LLT]
- Angiocentric lymphomas [MedDRA High Level Term]
- Extranodal NK/T-cell lymphoma, nasal type [MedDRA LLT]
- Extranodal NK/T-cell lymphoma, nasal type [ICD-10 Sub-category]
- Extranodal NK/T-cell lymphoma, nasal type [ICD-11 Subcategory]
- Extranodal natural killer/T-cell lymphoma, nasal type (disorder) [SNOMED CT concept]
- NK/T-cell lymphoma, nasal and nasal-type [ICD-O code]
- angiocentric lymphoma [Disease (Nov.)]
- extranodal NK-T-Cell lymphoma, nasal and Nasal-Type [MeSH concept]
Validated automatic mappings to NTBT
- angiocentric lymphoma [Disease (Nov.)]
concept_is_in_subset
- CDISC SEND Terminology [NCIt concept]
- CDISC SEND Tumor Findings Results Terminology [NCIt concept]
- CTRP Disease Terminology [NCIt concept]
- CTRP Terminology [NCIt concept]
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]
- Clinical Data Interchange Standards Consortium Terminology [NCIt concept]
- GDC Terminology [NCIt concept]
- GDC Value Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.1 Morphology Terminology [NCIt concept]
- Mapped ICDO3.1 Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology PT Terminology [NCIt concept]
- Mapped ICDO3.2 Morphology Terminology [NCIt concept]
- Mapped ICDO3.2 Terminology [NCIt concept]
- NCI CTEP SDC Non-Hodgkin Lymphoma Sub-Category Terminology [NCIt concept]
- NCI CTEP Simplified Disease Classification Terminology [NCIt concept]
- NCIt Neoplasm Core Terminology [NCIt concept]
- mCode Cancer Disorder Value Set [NCIt concept]
- mCode Elixhauser Lymphoma Value Set [NCIt concept]
- mCode Primary Cancer Disorder Value Set [NCIt concept]
- mCode Primary Malignant Neoplasm Disorder Value Set [NCIt concept]
- mCode Terminology [NCIt concept]
disease_excludes_finding
- Benign Cellular Infiltrate [NCIt concept]
disease_has_abnormal_cell
- Abnormal Lymphocyte [NCIt concept]
- Malignant Cell [NCIt concept]
- Neoplastic Cell [NCIt concept]
- Neoplastic Hematopoietic and Lymphoid Cell [NCIt concept]
- Neoplastic Lymphocyte [NCIt concept]
- Neoplastic T-Lymphocyte and Neoplastic Natural Killer Cell [NCIt concept]
disease_has_finding
- CD56-Positive Neoplastic Cells Present [NCIt concept]
- Extranodal Disease [NCIt concept]
- Malignant Cellular Infiltrate [NCIt concept]
disease_has_normal_cell_origin
- Hematopoietic and Lymphoid Cell [NCIt concept]
- Lymphocyte [NCIt concept]
- Peripheral (Post-Thymic) T-Lymphocyte and Natural Killer Cell [NCIt concept]
- T-Lymphocyte and Natural Killer Cell [NCIt concept]
disease_has_normal_tissue_origin
- Hematopoietic and Lymphoid Tissue [NCIt concept]
- Lymphoid Tissue [NCIt concept]
disease_has_primary_anatomic_site
- Hematopoietic and Lymphatic System [NCIt concept]
- Lymphatic System [NCIt concept]
disease_may_have_abnormal_cell
- Anaplastic Large T-Lymphocyte [NCIt concept]
- Neoplastic Large T-Lymphocyte [NCIt concept]
- Neoplastic Medium-Sized T-Lymphocyte [NCIt concept]
- Neoplastic Small T-Lymphocyte [NCIt concept]
- Neoplastic T-Immunoblast [NCIt concept]
disease_may_have_associated_disease
- Angiocentric Immunoproliferative Lesion [NCIt concept]
- EBV Infection [NCIt concept]
disease_may_have_cytogenetic_abnormality
- del(6q21q25) [NCIt concept]
disease_may_have_normal_cell_origin
- Activated Natural Killer Cell [NCIt concept]
- Cytotoxic T-Lymphocyte [NCIt concept]
may_be_associated_disease_of_disease
- Aggressive NK-Cell Leukemia [NCIt concept]
- Recurrent Aggressive NK-Cell Leukemia [NCIt concept]
- Refractory Aggressive NK-Cell Leukemia [NCIt concept]

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