" /> Infantile Fibrosarcoma - CISMeF





Preferred Label : Infantile Fibrosarcoma;

NCIt synonyms : Congenital Fibrosarcoma; IFS;

NCIt related terms : Infantile fibrosarcoma (congenital fibrosarcoma);

NCIt definition : A fibrosarcoma that occurs in infants. It shares identical morphologic features with adult fibrosarcoma but carries the t(12;15)(p13;q25) translocation that results in ETV6-NTRK3 gene fusion. It usually affects the superficial and deep soft tissues of the extremities. The prognosis is generally much more favorable than for adult fibrosarcoma, and it rarely metastasizes.;

Alternative definition : NICHD: A fibrosarcoma typically congenital, and occurring most commonly within the first three months of life, sharing identical morphologic features with adult fibrosarcoma but rarely metastatic. It usually affects the superficial and deep soft tissues of the extremities. The majority of infantile fibrosarcomas carry the t(12;15)(p13;q25) translocation.;

Neoplastic status : Malignant;

ICD-O code : 8814/3;

Codes from synonyms : 10065859;

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24/07/2025


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