" /> Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor - CISMeF





Preferred Label : Ewing Sarcoma/Peripheral Primitive Neuroectodermal Tumor;

NCIt synonyms : Ewing's Sarcoma/Peripheral Primitive Neuroectodermal Tumor; Ewing's Family of Tumours; Ewing Family of Tumors; Ewing's Family of Tumors; Tumors of the Ewing's Family; Tumors of Ewing's Family; Ewing s Sarcoma Peripheral Primitive Neuroectodermal Tumor;

NCIt related terms : Ewing sarcoma/Peripheral PNET; EFTs; Ewing sarcoma family of tumors;

NCIt definition : A spectrum of malignant tumors, affecting mostly males under age 20, characterized morphologically by the presence of small round cells. Ewing sarcoma and peripheral primitive neuroectodermal tumor represent the ends of a spectrum, with Ewing sarcoma lacking evidence of neural differentiation and the markers that characterize the peripheral primitive neuroectodermal tumor. Ewing sarcoma and peripheral primitive neuroectodermal tumor may share cytogenetic abnormalities, proto-oncogene expression, cell culture and immunohistochemical abnormalities. These tumors may occur in the soft tissues or the bones. Pain and the presence of a mass are the most common clinical symptoms.;

Alternative definition : NCI-GLOSS: A group of cancers that includes Ewing tumor of bone (ETB or Ewing sarcoma of bone), extraosseous Ewing (EOE) tumors, primitive neuroectodermal tumors (PNET or peripheral neuroepithelioma), and Askin tumors (PNET of the chest wall). These tumors all come from the same type of stem cell.;

Neoplastic status : Malignant;

Codes from synonyms : 10015563; CDR0000570758; CDR0000322134;

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11/11/2025


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