" /> dihydrolipoamide acyltransferase - CISMeF





Preferred Label : dihydrolipoamide acyltransferase;

MeSH note : component of branched-chain 2-oxo acid dehydrogenase multienzyme complex; mutation in this (E2) catalytic subunit identifies type II maple syrup urine disease; do not confuse with E2 enzymes of pyruvate dehydrogenase (PDC) and alpha-ketoglutarate dehydrogenase complexes;

MeSH synonym : dihydrolipoyl transacylase; branched chain acyltransferase; E2 transacylase; BCOADC-E2;

Registry Number MeSH : EC 2.3.1.-;

Is substance : O;

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27/07/2025


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