malignant atrophic papulosis

Preferred Label : malignant atrophic papulosis;

MeSH definition : Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown.;

MeSH synonym : degos disease; syndrome, degos; atrophic papuloses, malignant; atrophic papulosis, malignant; malignant atrophic papuloses; papuloses, malignant atrophic; papulosis, malignant atrophic; degos syndrome; disease, degos; kohlmeier-degos disease; disease, kohlmeier-degos; degos's malignant atrophic papulosis;

CISMeF synonym : kohlmeier degos disease; erythrokeratoderma en cocardes;

MeSH annotation : malignant does not refer to neoplasm; do not confuse with the neoplasm ACANTHOMA, DEGOS see ACANTHOMA;

Wikipedia link : https://en.wikipedia.org/wiki/Degos disease;

Details

Origin ID

D054853;

UMLS CUI

C0221011;

Allowable qualifiers
- blood [MeSH Qualifier]
- cerebrospinal fluid [MeSH Qualifier]
- chemically induced [MeSH Qualifier]
- classification [MeSH Qualifier]
- complications [MeSH Qualifier]
- congenital [MeSH Qualifier]
- diagnosis [MeSH Qualifier]
- diagnostic imaging [MeSH Qualifier]
- diet therapy [MeSH Qualifier]
- drug therapy [MeSH Qualifier]
- economics [MeSH Qualifier]
- embryology [MeSH Qualifier]
- enzymology [MeSH Qualifier]
- epidemiology [MeSH Qualifier]
- ethnology [MeSH Qualifier]
- etiology [MeSH Qualifier]
- genetics [MeSH Qualifier]
- history [MeSH Qualifier]
- immunology [MeSH Qualifier]
- metabolism [MeSH Qualifier]
- microbiology [MeSH Qualifier]
- mortality [MeSH Qualifier]
- nursing [MeSH Qualifier]
- parasitology [MeSH Qualifier]
- pathology [MeSH Qualifier]
- physiopathology [MeSH Qualifier]
- prevention and control [MeSH Qualifier]
- psychology [MeSH Qualifier]
- radiotherapy [MeSH Qualifier]
- rehabilitation [MeSH Qualifier]
- surgery [MeSH Qualifier]
- therapy [MeSH Qualifier]
- urine [MeSH Qualifier]
- veterinary [MeSH Qualifier]
- virology [MeSH Qualifier]
Currated CISMeF NLP mapping
- Degos disease [MedDRA LLT]
- Erythrokeratoderma ''en cocardes'' [ORDO Disease]
- Erythrokeratoderma en cocardes (disorder) [SNOMED CT concept]
- Kohlmeier-Degos syndrome [MedDRA LLT]
- Malignant Atrophic Papulosis [NCIt concept]
- Malignant atrophic papulosis [PASCAL descriptor]
- Malignant atrophic papulosis [ICD-11 More detail]
- Malignant atrophic papulosis [MedDRA Preferred Term]
- Malignant atrophic papulosis [OMIM Phenotype]
- Malignant atrophic papulosis [ORDO Disease]
- Malignant atrophic papulosis (disorder) [SNOMED CT concept]
- malignant atrophic papulosis [Disease (Nov.)]
- malignant atrophic papulosis [SNOMED Notion]
Manual NTBT mappings (CISMeF)
- Erythrokeratoderma [ORDO Disease]
- Genetic erythrokeratoderma [ORDO Disease]
- Genetic porokeratosis [ORDO Disease]
Ne pas confondre avec
- acanthoma [MeSH Descriptor]
ORDO relation(s)
- Malignant atrophic papulosis [ORDO Disease]
Record concept(s)
- Erythrokeratoderma en cocardes [MeSH concept]
- malignant atrophic papulosis [MeSH concept]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Degos disease [MedDRA LLT]
- Erythrokeratoderma ''en cocardes'' [ORDO Disease]
- Erythrokeratoderma en cocardes (disorder) [SNOMED CT concept]
- Kohlmeier-Degos syndrome [MedDRA LLT]
- Malignant Atrophic Papulosis [NCIt concept]
- Malignant atrophic papulosis [ORDO Disease]
- Malignant atrophic papulosis [OMIM Phenotype]
- Malignant atrophic papulosis [MedDRA Preferred Term]
- Malignant atrophic papulosis [PASCAL descriptor]
- Malignant atrophic papulosis (disorder) [SNOMED CT concept]
- malignant atrophic papulosis [SNOMED Notion]
- malignant atrophic papulosis [Disease (Nov.)]

Keyword's position in hierarchy(ies) :

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