Malignant Atrophic Papulosis

Preferred Label : Malignant Atrophic Papulosis;

NCIt synonyms : Degos Disease;

NCIt definition : A rare disorder of unknown etiology. It may present as a cutaneous disorder with a benign clinical course or a systemic disorder with a grim prognosis. Both the cutaneous and systemic variants are characterized by the presence of papular skin lesions. The systemic variant, in addition to the skin papules, is characterized by gastrointestinal manifestations including abdominal pain and distention, nausea, vomiting, diarrhea, intestinal infarction, and intestinal perforation. The central and peripheral nervous systems may also be involved in the systemic variant.;

Details

Origin ID

C84835;

UMLS CUI

C0221011;

Currated CISMeF NLP mapping
- Degos disease [MedDRA LLT]
- Erythrokeratoderma en cocardes (disorder) [SNOMED CT concept]
- Malignant atrophic papulosis [PASCAL descriptor]
- Malignant atrophic papulosis [ICD-11 More detail]
- Malignant atrophic papulosis [MedDRA Preferred Term]
- Malignant atrophic papulosis [OMIM Phenotype]
- Malignant atrophic papulosis [ORDO Disease]
- Malignant atrophic papulosis (disorder) [SNOMED CT concept]
- malignant atrophic papulosis [Disease (Nov.)]
- malignant atrophic papulosis [MeSH Descriptor]
- malignant atrophic papulosis [MeSH concept]
- malignant atrophic papulosis [SNOMED Notion]
See also inter- (CISMeF)
- Erythrokeratoderma ''en cocardes'' [ORDO Disease]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Degos disease [MedDRA LLT]
- Erythrokeratoderma ''en cocardes'' [ORDO Disease]
- Erythrokeratoderma en cocardes (disorder) [SNOMED CT concept]
- Kohlmeier-Degos syndrome [MedDRA LLT]
- Malignant atrophic papulosis [ORDO Disease]
- Malignant atrophic papulosis [OMIM Phenotype]
- Malignant atrophic papulosis [PASCAL descriptor]
- Malignant atrophic papulosis [MedDRA Preferred Term]
- Malignant atrophic papulosis (disorder) [SNOMED CT concept]
- malignant atrophic papulosis [Disease (Nov.)]
- malignant atrophic papulosis [MeSH concept]
- malignant atrophic papulosis [SNOMED Notion]
- malignant atrophic papulosis [MeSH Descriptor]
disease_has_finding
- Rare Lesion [NCIt concept]

Keyword's position in hierarchy(ies) :

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