aphasia, primary progressive

Preferred Label : aphasia, primary progressive;

MeSH definition : A progressive form of dementia characterized by the global loss of language abilities and initial preservation of other cognitive functions. Fluent and nonfluent subtypes have been described. Eventually a pattern of global cognitive dysfunction, similar to ALZHEIMER DISEASE, emerges. Pathologically, there are no Alzheimer or PICK DISEASE like changes, however, spongiform changes of cortical layers II and III are present in the TEMPORAL LOBE and FRONTAL LOBE. (From Brain 1998 Jan;121(Pt 1):115-26);

MeSH synonym : aphasias, primary progressive; primary progressive aphasia; progressive aphasia, primary; syndrome, mesulam's; syndrome, mesulam; mesulam syndrome; progressive aphasias, primary; primary progressive aphasias; mesulam's syndrome;

MeSH annotation : a clinical entity: do not confuse with descriptions of the progression of aphasia in case reports;

Wikipedia link : https://en.wikipedia.org/wiki/Primary progressive aphasia;

Details

Origin ID

D018888;

UMLS CUI

C0282513;

Allowable qualifiers
- blood [MeSH Qualifier]
- cerebrospinal fluid [MeSH Qualifier]
- chemically induced [MeSH Qualifier]
- classification [MeSH Qualifier]
- complications [MeSH Qualifier]
- diagnosis [MeSH Qualifier]
- diagnostic imaging [MeSH Qualifier]
- diet therapy [MeSH Qualifier]
- drug therapy [MeSH Qualifier]
- economics [MeSH Qualifier]
- enzymology [MeSH Qualifier]
- epidemiology [MeSH Qualifier]
- ethnology [MeSH Qualifier]
- etiology [MeSH Qualifier]
- genetics [MeSH Qualifier]
- history [MeSH Qualifier]
- immunology [MeSH Qualifier]
- metabolism [MeSH Qualifier]
- microbiology [MeSH Qualifier]
- mortality [MeSH Qualifier]
- nursing [MeSH Qualifier]
- parasitology [MeSH Qualifier]
- pathology [MeSH Qualifier]
- physiopathology [MeSH Qualifier]
- prevention and control [MeSH Qualifier]
- psychology [MeSH Qualifier]
- rehabilitation [MeSH Qualifier]
- surgery [MeSH Qualifier]
- therapy [MeSH Qualifier]
- urine [MeSH Qualifier]
- virology [MeSH Qualifier]
Automatic exact mappings (from CISMeF team)
- Frontotemporal dementia 2 [OMIM Phenotype]
- Frontotemporal dementia, language variant [ICD-11 More detail]
Currated CISMeF NLP mapping
- Primary Progressive Aphasia [NCIt concept]
- Primary progressive aphasia [MedDRA Preferred Term]
- Primary progressive aphasia [ORDO Disease]
- Primary progressive apraxia of speech (disorder) [SNOMED CT concept]
- primary progressive aphasia [Disease (Nov.)]
Manual BTNT mappings - CISMeF
- Semantic dementia [ORDO Disease]
Manual NTBT mappings (CISMeF)
- Frontotemporal degeneration with dementia [ORDO Disease]
- Rare dementia [ORDO Disease]
ORDO relation(s)
- Primary progressive aphasia [ORDO Disease]
Record concept(s)
- aphasia, primary progressive [MeSH concept]
See also
- alzheimer disease [MeSH Descriptor]
Semantic type(s)
- Mental or Behavioral Dysfunction [UMLS semantic type]
UMLS correspondences (same concept)
- Primary Progressive Aphasia [NCIt concept]
- Primary progressive aphasia [ORDO Disease]
- Primary progressive aphasia [MedDRA Preferred Term]
- Primary progressive apraxia of speech (disorder) [SNOMED CT concept]
- primary progressive aphasia [Disease (Nov.)]

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