Preferred Label : Frontotemporal dementia, language variant;
ICD-11 definition : A clinical syndrome primarily affecting language. It is characterised by an insidious
onset and gradual progressive impairment of language that affects activities of daily
living. Aphasia should be the most prominent deficit during the initial phases of
the disease. As the clinical syndrome progresses, other cognitive functions may be
involved as well, but language remains the most impaired domain throughout the disease.;
ICD-11 synonym : Progressive aphasia; Primary progressive aphasia;
Origin ID : 1693157226;
Automatic exact mappings (from CISMeF team)
A clinical syndrome primarily affecting language. It is characterised by an insidious
onset and gradual progressive impairment of language that affects activities of daily
living. Aphasia should be the most prominent deficit during the initial phases of
the disease. As the clinical syndrome progresses, other cognitive functions may be
involved as well, but language remains the most impaired domain throughout the disease.
