Preferred Label : sarcoma, alveolar soft part;
MeSH definition : A variety of rare sarcoma having a reticulated fibrous stroma enclosing groups of
sarcoma cells, which resemble epithelial cells and are enclosed in alveoli walled
with connective tissue. It is a rare tumor, usually occurring between 15 and 35 years
of age. It appears in the muscles of the extremities in adults and most commonly in
the head and neck regions of children. Though slow-growing, it commonly metastasizes
to the lungs, brain, bones, and lymph nodes. (DeVita Jr et al., Cancer: Principles
& Practice of Oncology, 3d ed, p1365);
MeSH synonym : alveolar soft part sarcoma; alveolar Soft-Part sarcoma;
MeSH annotation : alveolar has nothing to do with pulm alveoli: it refers to sac-like pathol of soft
part; /blood /chem /second /secret /ultrastruct permitted; coord IM with precoord
organ/neopl term (IM); alveolar has nothing to do with pulmonary alveoli: it refers to sac-like pathology
of soft part; coordinate with precoordinated organ/neoplasm term;
Wikipedia link : https://en.wikipedia.org/wiki/Alveolar soft part sarcoma;
Origin ID : D018234;
UMLS CUI : C0206657;
Allowable qualifiers
- Automatic exact mappings (from CISMeF team)
- Currated CISMeF NLP mapping
- DO Cross reference
- HPO term
- Manual NTBT mappings (CISMeF)
- ORDO relation(s)
- Record concept(s)
- Semantic type(s)
- UMLS correspondences (same concept)
A variety of rare sarcoma having a reticulated fibrous stroma enclosing groups of
sarcoma cells, which resemble epithelial cells and are enclosed in alveoli walled
with connective tissue. It is a rare tumor, usually occurring between 15 and 35 years
of age. It appears in the muscles of the extremities in adults and most commonly in
the head and neck regions of children. Though slow-growing, it commonly metastasizes
to the lungs, brain, bones, and lymph nodes. (DeVita Jr et al., Cancer: Principles
& Practice of Oncology, 3d ed, p1365)
http://www.orpha.net/consor/cgi-bin/OC_Exp.php?Lng=FR&Expert=163699
2011
France
scientific and technical information
sarcoma, alveolar soft part
sarcoma, alveolar soft part
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