NCIt related terms : ASPS; Alveolar soft-part sarcoma;
NCIt definition : A rare malignant neoplasm characterized by the presence of large epithelioid cells
with abundant cytoplasm forming nests and pseudoalveolar structures. The groups of
the epithelioid cells are separated by thin-walled sinusoidal spaces. It occurs most
often in adolescents and young adults. In adults the most common sites of involvement
are the extremities, and in infants and children, the head and neck. It usually presents
as a slowly growing mass and it frequently metastasizes to other anatomic sites. The
most common sites of metastasis are the lungs, bone, and brain.;
Alternative definition : NCI-GLOSS: A soft tissue tumor that is most common in older children and teenagers.
It begins in the soft supporting tissue that connects and surrounds the organs and
other tissues. Alveolar soft part sarcoma usually occurs in the legs, but can also
occur in the arms, hands, head, or neck. It can cause the growth of new blood vessels
that help the tumor grow and spread.;
Neoplastic status : Malignant;
ICD-O code : 9581/3;
Codes from synonyms : CDR0000641934; CDR0000641933; 10001886;