dermatofibrosarcoma

Preferred Label : dermatofibrosarcoma;

MeSH definition : A sarcoma of the deep layers of the skin. The tumors are locally aggressive tends to recur but rarely metastatic. It can be classified into variants depending on the cell type tumors are derived from or by its characteristics: Pigmented variant from MELANIN-containing DERMAL DENDRITIC CELLS; Myxoid variant, myxoid STROMAL CELLS; Giant cell variant characterized by GIANT CELLS in the tumors; and Fibrosarcomatous variant chracterized by tumor areas histologically indistinguishable from FIBROSARCOMA.;

MeSH synonym : dermatofibrosarcomas; Darier-Hoffmann tumor; Darier-Ferrand tumor; Darier Hoffmann Tumor; Tumor, Darier-Hoffmann; Dermatofibrosarcoma Protuberan; Dermatofibrosarcoma Protuberans; Protuberan, Dermatofibrosarcoma; Protuberans, Dermatofibrosarcoma; Darier Ferrand Tumor; Tumor, Darier-Ferrand;

MeSH hyponym : Dermatofibrosarcoma Protuberans, Pigmented; Dermatofibrosarcoma Protuberans, Myxoid; Giant Cell Fibroblastoma; Metastatic Dermatofibrosarcoma Protuberans; Dermatofibrosarcoma Protuberan, Metastatic; Dermatofibrosarcoma Protuberans, Metastatic; Metastatic Dermatofibrosarcoma Protuberan; Protuberan, Metastatic Dermatofibrosarcoma; Protuberans, Metastatic Dermatofibrosarcoma; FS-DFSP; Fibrosarcomatous Dermatofibrosarcoma Protuberans; Dermatofibrosarcoma Protuberans, Fibrosarcomatous; Dermatofibrosarcoma Protuberan, Fibrosarcomatous; Fibrosarcomatous Dermatofibrosarcoma Protuberan; Protuberan, Fibrosarcomatous Dermatofibrosarcoma; Protuberans, Fibrosarcomatous Dermatofibrosarcoma; DFSP, Fibrosarcomatous; DFSPs, Fibrosarcomatous; Fibrosarcomatous DFSP; Fibrosarcomatous DFSPs; Cell Fibroblastoma, Giant; Cell Fibroblastomas, Giant; Fibroblastoma, Giant Cell; Fibroblastomas, Giant Cell; Giant Cell Fibroblastomas; Giant Dermatofibrosarcoma Protuberans; Dermatofibrosarcoma Protuberan, Giant; Dermatofibrosarcoma Protuberans, Giant; Giant Dermatofibrosarcoma Protuberan; Protuberan, Giant Dermatofibrosarcoma; Protuberans, Giant Dermatofibrosarcoma; DFSP, Juvenile; DFSPs, Juvenile; Juvenile DFSP; Juvenile DFSPs; Familial Dermatofibrosarcoma Protuberans; Dermatofibrosarcoma Protuberans, Familial; Dermatofibrosarcoma Protuberan, Familial; Familial Dermatofibrosarcoma Protuberan; Protuberan, Familial Dermatofibrosarcoma; Protuberans, Familial Dermatofibrosarcoma; Dermatofibrosarcoma Protuberans, Giant Cell; Dermatofibrosarcoma Protuberan, Myxoid; Myxoid Dermatofibrosarcoma Protuberan; Myxoid Dermatofibrosarcoma Protuberans; Protuberan, Myxoid Dermatofibrosarcoma; Protuberans, Myxoid Dermatofibrosarcoma; DFSP, Myxoid; DFSPs, Myxoid; Myxoid DFSP; Myxoid DFSPs; Dermatofibrosarcoma Protuberan, Pigmented; Pigmented Dermatofibrosarcoma Protuberan; Pigmented Dermatofibrosarcoma Protuberans; Protuberan, Pigmented Dermatofibrosarcoma; Protuberans, Pigmented Dermatofibrosarcoma; Bednar's Tumor; Bednars Tumor; Tumor, Bednar's; DFSP, Pigmented; DFSPs, Pigmented; Pigmented DFSP; Pigmented DFSPs; Bednar Tumor; Tumor, Bednar;

MeSH annotation : /blood supply /chem /second /secret /ultrastruct permitted; coord IM with SKIN NEOPLASMS (IM); coordinate with with SKIN NEOPLASMS;

Wikipedia link : https://en.wikipedia.org/wiki/Dermatofibrosarcoma protuberans;

Details

Origin ID

D018223;

UMLS CUI

C0206647;

Allowable qualifiers
- blood [MeSH Qualifier]
- blood supply [MeSH Qualifier]
- cerebrospinal fluid [MeSH Qualifier]
- chemically induced [MeSH Qualifier]
- chemistry [MeSH Qualifier]
- classification [MeSH Qualifier]
- complications [MeSH Qualifier]
- congenital [MeSH Qualifier]
- diagnosis [MeSH Qualifier]
- diagnostic imaging [MeSH Qualifier]
- diet therapy [MeSH Qualifier]
- drug therapy [MeSH Qualifier]
- economics [MeSH Qualifier]
- embryology [MeSH Qualifier]
- enzymology [MeSH Qualifier]
- epidemiology [MeSH Qualifier]
- ethnology [MeSH Qualifier]
- etiology [MeSH Qualifier]
- genetics [MeSH Qualifier]
- history [MeSH Qualifier]
- immunology [MeSH Qualifier]
- metabolism [MeSH Qualifier]
- microbiology [MeSH Qualifier]
- mortality [MeSH Qualifier]
- nursing [MeSH Qualifier]
- parasitology [MeSH Qualifier]
- pathology [MeSH Qualifier]
- physiopathology [MeSH Qualifier]
- prevention and control [MeSH Qualifier]
- psychology [MeSH Qualifier]
- radiotherapy [MeSH Qualifier]
- rehabilitation [MeSH Qualifier]
- secondary [MeSH Qualifier]
- surgery [MeSH Qualifier]
- therapy [MeSH Qualifier]
- ultrastructure [MeSH Qualifier]
- urine [MeSH Qualifier]
- veterinary [MeSH Qualifier]
- virology [MeSH Qualifier]
Automatic exact mappings (from CISMeF team)
- Dermatofibrosarcoma [PASCAL descriptor]
- Dermatofibrosarcoma protuberans [ICD-11 More detail]
- Dermatofibrosarcoma protuberans metastatic [MedDRA Preferred Term]
- Dermatofibrosarcoma protuberans, fibrosarcomatous [ICD-11 Extension code]
- Dermatofibrosarcoma, NOS [ICD-O code]
- Fibrosarcomatous Dermatofibrosarcoma Protuberans [NCIt concept]
- Fibrosarcomatous dermatofibrosarcoma protuberans (morphologic abnormality) [SNOMED CT concept]
- Giant cell fibroblastoma [ICD-11 Extension code]
- Giant cell fibroblastoma [ICD-O code]
- Myxoid Dermatofibrosarcoma Protuberans [NCIt concept]
- Myxoid dermatofibrosarcoma protuberans (disorder) [SNOMED CT concept]
- Pigmented Dermatofibrosarcoma Protuberans [NCIt concept]
- Pigmented dermatofibrosarcoma protuberans [ICD-O code]
- Pigmented dermatofibrosarcoma protuberans [ICD-11 Extension code]
- Pigmented dermatofibrosarcoma protuberans (morphologic abnormality) [SNOMED CT concept]
- Pigmented dermatofibrosarcoma protuberans of skin (disorder) [SNOMED CT concept]
- pigmented dermatofibrosarcoma protuberans [SNOMED Notion]
Currated CISMeF NLP mapping
- Dermatofibrosarcoma [MedDRA LLT]
- Dermatofibrosarcoma (morphologic abnormality) [SNOMED CT concept]
- Dermatofibrosarcoma Protuberans [NCIt concept]
- Dermatofibrosarcoma protuberans [OMIM Phenotype]
- Dermatofibrosarcoma protuberans [MedDRA Preferred Term]
- Dermatofibrosarcoma protuberans [ORDO Disease]
- Dermatofibrosarcoma protuberans [PASCAL descriptor]
- Giant Cell Fibroblastoma [NCIt concept]
- Giant cell fibroblastoma (morphologic abnormality) [SNOMED CT concept]
- Giant cell fibroblastoma of skin (disorder) [SNOMED CT concept]
- dermatofibrosarcoma protuberans [DO Concept]
- dermatofibrosarcoma protuberans [Disease (Nov.)]
- dermatofibrosarcoma, nos [SNOMED Notion]
DO Cross reference
- dermatofibrosarcoma protuberans [DO Concept]
False UMLS correspondences (reviewed by CISMeF team)
- Dermatofibrosarcoma protuberans (disorder) [SNOMED CT concept]
False automatic mappings
- Dermatofibrosarcoma protuberans (disorder) [SNOMED CT concept]
Record concept(s)
- Dermatofibrosarcoma Protuberans, Myxoid [MeSH concept]
- Dermatofibrosarcoma Protuberans, Pigmented [MeSH concept]
- Giant Cell Fibroblastoma [MeSH concept]
- Metastatic Dermatofibrosarcoma Protuberans [MeSH concept]
- dermatofibrosarcoma [MeSH concept]
Semantic type(s)
- Neoplastic Process [UMLS semantic type]
UMLS correspondences (same concept)
- Dermatofibrosarcoma [MedDRA LLT]
- dermatofibrosarcoma protuberans [DO Concept]
- dermatofibrosarcoma, nos [SNOMED Notion]

Keyword's position in hierarchy(ies) :

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