NCIt definition : A rare, locally aggressive fibroblastic neoplasm typically affecting young patients
(predominantly boys). It manifests with painless nodules in the dermis or subcutaneous
tissues. Morphologically, it contains giant cells and wide vessel-like spaces. This
tumor can recur but metastases have not been reported.;
Alternative definition : NCI-GLOSS: A rare type of soft tissue tumor marked by painless nodules in the dermis
(the inner layer of the two main layers of tissue that make up the skin) and subcutaneous
(beneath the skin) tissue. These tumors may come back after surgery, but they do not
spread to other parts of the body. They occur mostly in boys and are related to dermatofibrosarcoma
protuberans.;