subacute sclerosing panencephalitis

Preferred Label : subacute sclerosing panencephalitis;

MeSH definition : A rare, slowly progressive encephalitis caused by chronic infection with the MEASLES VIRUS. The condition occurs primarily in children and young adults, approximately 2-8 years after the initial infection. A gradual decline in intellectual abilities and behavioral alterations are followed by progressive MYOCLONUS; MUSCLE SPASTICITY; SEIZURES; DEMENTIA; autonomic dysfunction; and ATAXIA. DEATH usually occurs 1-3 years after disease onset. Pathologic features include perivascular cuffing, eosinophilic cytoplasmic inclusions, neurophagia, and fibrous gliosis. It is caused by the SSPE virus, which is a defective variant of MEASLES VIRUS. (From Adams et al., Principles of Neurology, 6th ed, pp767-8);

MeSH synonym : panencephalitides, subacute sclerosing; sclerosing panencephalitides, subacute; subacute sclerosing panencephalitides; leukoencephalitis, van bogaert's; leukoencephalitis, van bogaert; leukoencephalitis, van bogaerts; inclusion body encephalitis, measles; sclerosing leukoencephalitis, subacute; leukoencephalitides, subacute sclerosing; subacute sclerosing leukoencephalitides; subacute sclerosing leukoencephalitis; sspe; van bogaert's leukoencephalitis; measles inclusion body encephalitis; sclerosing leukoencephalitides, subacute; van bogaerts leukoencephalitis; leukoencephalitis, subacute sclerosing; panencephalitis, subacute sclerosing; van bogaert leukoencephalitis; sclerosing panencephalitis, subacute; Encephalitis, Inclusion Body, Measles;

CISMeF synonym : encephaltis, inclusion body, measles;

Wikipedia link : https://en.wikipedia.org/wiki/Subacute sclerosing panencephalitis;

Details

Origin ID

D013344;

UMLS CUI

C0038522;

Allowable qualifiers
- blood [MeSH Qualifier]
- cerebrospinal fluid [MeSH Qualifier]
- chemically induced [MeSH Qualifier]
- classification [MeSH Qualifier]
- complications [MeSH Qualifier]
- congenital [MeSH Qualifier]
- diagnosis [MeSH Qualifier]
- diagnostic imaging [MeSH Qualifier]
- diet therapy [MeSH Qualifier]
- drug therapy [MeSH Qualifier]
- economics [MeSH Qualifier]
- embryology [MeSH Qualifier]
- enzymology [MeSH Qualifier]
- epidemiology [MeSH Qualifier]
- ethnology [MeSH Qualifier]
- etiology [MeSH Qualifier]
- genetics [MeSH Qualifier]
- history [MeSH Qualifier]
- immunology [MeSH Qualifier]
- metabolism [MeSH Qualifier]
- microbiology [MeSH Qualifier]
- mortality [MeSH Qualifier]
- nursing [MeSH Qualifier]
- parasitology [MeSH Qualifier]
- pathology [MeSH Qualifier]
- physiopathology [MeSH Qualifier]
- prevention and control [MeSH Qualifier]
- psychology [MeSH Qualifier]
- radiotherapy [MeSH Qualifier]
- rehabilitation [MeSH Qualifier]
- surgery [MeSH Qualifier]
- therapy [MeSH Qualifier]
- transmission [MeSH Qualifier]
- urine [MeSH Qualifier]
- veterinary [MeSH Qualifier]
- virology [MeSH Qualifier]
Currated CISMeF NLP mapping
- Measles inclusion body encephalitis (disorder) [SNOMED CT concept]
- Subacute Sclerosing Panencephalitis [NCIt concept]
- Subacute sclerosing leukoencephalitis [ORDO Disease]
- Subacute sclerosing panencephalitis [ICD-10 Sub-category]
- Subacute sclerosing panencephalitis [ICD-10 Sub-category (who)]
- Subacute sclerosing panencephalitis [MedDRA Preferred Term]
- Subacute sclerosing panencephalitis [ICD-11 Sub-sub category]
- Subacute sclerosing panencephalitis [ICD-9 code]
- Subacute sclerosing panencephalitis [OMIM Phenotype]
- Subacute sclerosing panencephalitis (disorder) [SNOMED CT concept]
- Van Bogaert's sclerosing leukoencephalitis (disorder) [SNOMED CT concept]
- subacute sclerosing panencephalitis [TUV Concept]
- subacute sclerosing panencephalitis [TUV Term]
- subacute sclerosing panencephalitis [DO Concept]
- subacute sclerosing panencephalitis [Disease (Nov.)]
- subacute sclerosing panencephalitis [SNOMED Notion]
DO Cross reference
- subacute sclerosing panencephalitis [DO Concept]
Manual NTBT mappings (CISMeF)
- Chronic encephalitis [ORDO Disease]
- Infectious disease with epilepsy [ORDO Disease]
Record concept(s)
- subacute sclerosing panencephalitis [MeSH concept]
Related MeSH Supplementary Concept(s)
- polycystic lipomembranous osteodysplasia with sclerosing leukoencephalopathy [MeSH Supplementary Concept]
See also
- measles virus [MeSH Descriptor]
See also (suggested by CISMeF)
- sspe virus [MeSH Descriptor]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Measles inclusion body encephalitis (disorder) [SNOMED CT concept]
- Subacute Sclerosing Panencephalitis [NCIt concept]
- Subacute sclerosing leukoencephalitis [ORDO Disease]
- Subacute sclerosing panencephalitis [ICD-9 code]
- Subacute sclerosing panencephalitis [OMIM Phenotype]
- Subacute sclerosing panencephalitis [ICD-10 Sub-category]
- Subacute sclerosing panencephalitis [MedDRA Preferred Term]
- Subacute sclerosing panencephalitis [ICD-10 Sub-category (who)]
- Subacute sclerosing panencephalitis [ICD-11 Sub-sub category]
- Subacute sclerosing panencephalitis (disorder) [SNOMED CT concept]
- Van Bogaert encephalitis [MedDRA LLT]
- Van Bogaert's sclerosing leukoencephalitis (disorder) [SNOMED CT concept]
- subacute sclerosing panencephalitis [TUV Concept]
- subacute sclerosing panencephalitis [TUV Term]
- subacute sclerosing panencephalitis [SNOMED Notion]
- subacute sclerosing panencephalitis [DO Concept]
- subacute sclerosing panencephalitis [Disease (Nov.)]

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