Subacute Sclerosing Panencephalitis

Preferred Label : Subacute Sclerosing Panencephalitis;

NCIt related terms : SSPE;

NCIt definition : A rare, slowly progressive post-infectious neurological disorder affecting the central nervous system. It is characterized by seizures, ataxia, myoclonus, personality changes, spasticity, and coma. The symptoms appear several years following measles infection at an early age.;

Alternative definition : NICHD: An encephalitic disorder that occurs following a measles infection. The disease initially manifests as personality changes, and then progresses to muscle spasms and seizures, possibly death.;

Details

Origin ID

C85171;

UMLS CUI

C0038522;

Automatic exact mappings (from CISMeF team)
- Encephalitis, myelitis, and encephalomyelitis in rickettsial diseases classified elsewhere [ICD-9 code]
- evoked potentials, somatosensory [MeSH Descriptor]
CISMeF manual mappings
- Van Bogaert's sclerosing leukoencephalitis (disorder) [SNOMED CT concept]
Currated CISMeF NLP mapping
- Measles inclusion body encephalitis (disorder) [SNOMED CT concept]
- Subacute sclerosing leukoencephalitis [ORDO Disease]
- Subacute sclerosing panencephalitis [OMIM Phenotype]
- Subacute sclerosing panencephalitis [ICD-9 code]
- Subacute sclerosing panencephalitis [ICD-10 Sub-category]
- Subacute sclerosing panencephalitis [ICD-11 Sub-sub category]
- Subacute sclerosing panencephalitis [ICD-10 Sub-category (who)]
- Subacute sclerosing panencephalitis [MedDRA Preferred Term]
- Subacute sclerosing panencephalitis (disorder) [SNOMED CT concept]
- subacute sclerosing panencephalitis [DO Concept]
- subacute sclerosing panencephalitis [Disease (Nov.)]
- subacute sclerosing panencephalitis [MeSH Descriptor]
- subacute sclerosing panencephalitis [MeSH concept]
- subacute sclerosing panencephalitis [SNOMED Notion]
- subacute sclerosing panencephalitis [TUV Concept]
- subacute sclerosing panencephalitis [TUV Term]
DO Cross reference
- subacute sclerosing panencephalitis [DO Concept]
Has associated anatomic sites
- Central Nervous System [NCIt concept]
- Nervous System [NCIt concept]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Measles inclusion body encephalitis (disorder) [SNOMED CT concept]
- Subacute sclerosing leukoencephalitis [ORDO Disease]
- Subacute sclerosing panencephalitis [ICD-9 code]
- Subacute sclerosing panencephalitis [OMIM Phenotype]
- Subacute sclerosing panencephalitis [ICD-10 Sub-category]
- Subacute sclerosing panencephalitis [ICD-11 Sub-sub category]
- Subacute sclerosing panencephalitis [ICD-10 Sub-category (who)]
- Subacute sclerosing panencephalitis [MedDRA Preferred Term]
- Subacute sclerosing panencephalitis (disorder) [SNOMED CT concept]
- Van Bogaert encephalitis [MedDRA LLT]
- Van Bogaert's sclerosing leukoencephalitis (disorder) [SNOMED CT concept]
- subacute sclerosing panencephalitis [TUV Concept]
- subacute sclerosing panencephalitis [TUV Term]
- subacute sclerosing panencephalitis [DO Concept]
- subacute sclerosing panencephalitis [Disease (Nov.)]
- subacute sclerosing panencephalitis [MeSH concept]
- subacute sclerosing panencephalitis [SNOMED Notion]
- subacute sclerosing panencephalitis [MeSH Descriptor]
concept_is_in_subset
- Cellosaurus Disease Terminology [NCIt concept]
- Cellosaurus Terminology [NCIt concept]
- NICHD Terminology [NCIt concept]
- Pediatric Adverse Events Terminology [NCIt concept]
- Pediatric Adverse Events Terminology Mapped to MedDRA [NCIt concept]
- Pediatric Infectious Disease Terminology [NCIt concept]
disease_has_finding
- Rare Lesion [NCIt concept]
disease_has_primary_anatomic_site
- Brain [NCIt concept]

Keyword's position in hierarchy(ies) :

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