scimitar syndrome

Preferred Label : scimitar syndrome;

MeSH definition : An anomalous pulmonary venous return in which the right PULMONARY VEIN is not connected to the LEFT ATRIUM but to the INFERIOR VENA CAVA. Scimitar syndrome is named for the crescent- or Turkish sword-like shadow in the chest radiography and is often associated with hypoplasia of the right lung and right pulmonary artery, and dextroposition of the heart.;

MeSH synonym : scimitar anomaly; anomaly, scimitar;

CISMeF synonym : anomalous pulmonary venous return; syndrome, scimitar; total anomalous pulmonary venous return; total anomalous pulmonary venous return 1;

MeSH hyponym : TAPVR1; TAPVR;

Related MeSH term : Pulmonary Venous Return Anomaly;

Wikipedia link : https://en.wikipedia.org/wiki/Anomalous pulmonary venous return;

Details

Origin ID

D012587;

UMLS CUI

C0036400;

Allowable qualifiers
- blood [MeSH Qualifier]
- cerebrospinal fluid [MeSH Qualifier]
- chemically induced [MeSH Qualifier]
- classification [MeSH Qualifier]
- complications [MeSH Qualifier]
- diagnosis [MeSH Qualifier]
- diagnostic imaging [MeSH Qualifier]
- diet therapy [MeSH Qualifier]
- drug therapy [MeSH Qualifier]
- economics [MeSH Qualifier]
- embryology [MeSH Qualifier]
- enzymology [MeSH Qualifier]
- epidemiology [MeSH Qualifier]
- ethnology [MeSH Qualifier]
- etiology [MeSH Qualifier]
- genetics [MeSH Qualifier]
- history [MeSH Qualifier]
- immunology [MeSH Qualifier]
- metabolism [MeSH Qualifier]
- microbiology [MeSH Qualifier]
- mortality [MeSH Qualifier]
- nursing [MeSH Qualifier]
- parasitology [MeSH Qualifier]
- pathology [MeSH Qualifier]
- physiopathology [MeSH Qualifier]
- prevention and control [MeSH Qualifier]
- psychology [MeSH Qualifier]
- radiotherapy [MeSH Qualifier]
- rehabilitation [MeSH Qualifier]
- surgery [MeSH Qualifier]
- therapy [MeSH Qualifier]
- urine [MeSH Qualifier]
- veterinary [MeSH Qualifier]
- virology [MeSH Qualifier]
Automatic exact mappings (from CISMeF team)
- Anomalous pulmonary venous connection, unspecified [ICD-10 Sub-category (who)]
- Anomaly of great veins, unspecified [ICD-9 code]
- Cardiac total anomalous pulmonary venous connection [HPO term]
- Other congenital malformations of great veins [ICD-10 Sub-category]
- Other congenital malformations of great veins [ICD-10 Sub-category (who)]
- Scimitar syndrome [PASCAL descriptor]
- Scimitar syndrome [ICD-11 Sub-sub category]
- Total Anomalous Pulmonary Venous Return [NCIt concept]
- Total anomalous pulmonary venous connection [ICD-10 Sub-category (who)]
- Total anomalous pulmonary venous connection [ICD-10 Sub-category]
- Total anomalous pulmonary venous connection [MedDRA LLT]
- Total anomalous pulmonary venous connection [ICD-11 Sub-sub category]
- Total anomalous pulmonary venous return [HPO term]
- Total anomalous pulmonary venous return (disorder) [SNOMED CT concept]
- scimitar syndrome [DO Concept]
- total anomalous pulmonary venous return [SNOMED Notion]
- total anomalous pulmonary venous return [Radlex concept]
CISMeF manual mappings
- Scimitar anomaly [HPO term]
Currated CISMeF NLP mapping
- Anomalous pulmonary venous drainage [PASCAL descriptor]
- Anomalous pulmonary venous drainage (disorder) [SNOMED CT concept]
- Anomalous pulmonary venous return [HPO term]
- Anomalous pulmonary venous return [HRDO Sign]
- Scimitar Syndrome [NCIt concept]
- Scimitar syndrome [MedDRA Preferred Term]
- Scimitar syndrome [ORDO Disease]
- Scimitar syndrome (disorder) [SNOMED CT concept]
- Total anomalous pulmonary venous return 1 [OMIM Phenotype]
- anomalous pulmonary venous drainage, nos [SNOMED Notion]
- scimitar syndrome [SNOMED Notion]
DO Cross reference
- scimitar syndrome [DO Concept]
HPO term
- Anomalous pulmonary venous return [HPO term]
- Scimitar anomaly [HPO term]
- Total anomalous pulmonary venous return [HPO term]
Manual NTBT mappings (CISMeF)
- Congenital pulmonary venous return anomaly [ORDO Disease]
ORDO relation(s)
- Scimitar syndrome [ORDO Disease]
Record concept(s)
- Anomalous Pulmonary Venous Return [MeSH concept]
- Total Anomalous Pulmonary Venous Return [MeSH concept]
- Total Anomalous Pulmonary Venous Return 1 [MeSH concept]
- scimitar syndrome [MeSH concept]
Related MeSH Supplementary Concept(s)
- scimitar anomaly, multiple cardiac malformations, and craniofacial and central nervous system abnormalities [MeSH Supplementary Concept]
Semantic type(s)
- Disease or Syndrome [UMLS semantic type]
UMLS correspondences (same concept)
- Anomalous pulmonary venous return [HPO term]
- Scimitar Syndrome [NCIt concept]
- Scimitar anomaly [HPO term]
- Scimitar syndrome [ORDO Disease]
- Scimitar syndrome [MedDRA Preferred Term]
- Scimitar syndrome (disorder) [SNOMED CT concept]
- Total anomalous pulmonary venous return [HPO term]
- Total anomalous pulmonary venous return 1 [OMIM Phenotype]
- scimitar syndrome [DO Concept]
- scimitar syndrome [SNOMED Notion]
- total anomalous pulmonary venous return [SNOMED Notion]

Keyword's position in hierarchy(ies) :

Main resources

You can consult :

recommendations
documents concerning education
documents for patients