Scimitar syndrome

ICD-11 code : LA86.22;

Preferred Label : Scimitar syndrome;

ICD-11 definition : A congenital cardiopulmonary malformation with partial anomalous pulmonary venous connection of Scimitar type and one or more of the following: hypoplasia of the right lung with bronchial anomalies, dextrocardia, hypoplasia of the right pulmonary artery, lobar lung sequestration, and anomalous systemic arterial supply to the lower lobe of the right lung directly from the aorta or its main branches.;

ICD-11 synonym : pulmonary venolobar syndrome;

Details

Origin ID

1321054364;

Automatic exact mappings (from CISMeF team)
- Other congenital malformations of great veins [ICD-10 Sub-category]
- Scimitar Syndrome [NCIt concept]
- Scimitar anomaly [HPO term]
- Scimitar syndrome [ORDO Disease]
- Scimitar syndrome [PASCAL descriptor]
- Scimitar syndrome [MedDRA Preferred Term]
- Scimitar syndrome (disorder) [SNOMED CT concept]
- Total anomalous pulmonary venous return 1 [OMIM Phenotype]
- scimitar syndrome [SNOMED Notion]
- scimitar syndrome [MeSH concept]
- scimitar syndrome [DO Concept]
- scimitar syndrome [MeSH Descriptor]
ICD-10 Mapping
- Anomalous pulmonary venous connection, unspecified [ICD-10 Sub-category]

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