MeSH definition : A specific monosialoganglioside that accumulates abnormally within the nervous system
due to a deficiency of GM1-b-galactosidase, resulting in GM1 gangliosidosis.;
A specific monosialoganglioside that accumulates abnormally within the nervous system
due to a deficiency of GM1-b-galactosidase, resulting in GM1 gangliosidosis.