Primary biliary cholangitis

ICD-11 code : DB96.1;

Preferred Label : Primary biliary cholangitis;

ICD-11 definition : Primary biliary cholangitis is characterized by progressive destruction and disappearance of the intralobularbile duct epithelial cells leading to cholestasis (high alkaline phosphatase and GGT {gamma glutamyl transferase}) and eventually liver cirrhosis and liver failure, generally associated with the presence of circulating antimitochondrial antibodies and an increase of serum IgM levels.;

ICD-11 synonym : Tannhauser-Magendantz syndrome; Mahon-Tannhauser syndrome; Hanot-Rossle syndrome; Todd cirrhosis; monolobular cirrhosis; xanthomatous biliary cirrhosis.; Hanot syndrome; toxic cirrhosis; Charcot cirrhosis; pericholangiolic biliary cirrhosis; chronic nonsuppurative destructive cholangitis; primary biliary cirrhosis; Hanot cirrhosis; hypertrophic cirrhosis; hypertrophic biliary cirrhosis;

ICD-11 inclusion : unilobar cirrhosis; chronic nonsuppurative destructive cholangitis;

ICD-11 "other" category code : DB96.1Y;

ICD-11 "unspecified" category code : DB96.1Z;

Origin ID

649193479;

Automatic exact mappings (from CISMeF team)
- Biliary cirrhosis, primary [OMIM phenotypic series]
- Charcot's cirrhosis [MedDRA LLT]
- Hanot's cirrhosis [MedDRA LLT]
- Hypertrophic cirrhosis [MedDRA LLT]
- Todd's cirrhosis [MedDRA LLT]
- Toxic cirrhosis (disorder) [SNOMED CT concept]
Currated CISMeF NLP mapping
- Biliary cirrhosis [HPO term]
- Biliary cirrhosis (disorder) [SNOMED CT concept]
- Biliary cirrhosis primary [MedDRA Preferred Term]
- Biliary cirrhosis primary [MedDRA LLT]
- Chronic non-suppurative destructive cholangitis [MedDRA LLT]
- Primary Biliary Cholangitis [MeSH concept]
- Primary Biliary Cirrhosis [NCIt concept]
- Primary biliary cholangitis [ORDO Disease]
- Primary biliary cholangitis [MedDRA Preferred Term]
- Primary biliary cholangitis (disorder) [SNOMED CT concept]
- Primary biliary cirrhosis [ICD-10 Sub-category]
- Primary biliary cirrhosis [PASCAL descriptor]
- Primary biliary cirrhosis [MedDRA LLT]
- liver cirrhosis, biliary [MeSH Descriptor]
- primary biliary cholangitis [DO Concept]
- primary biliary cirrhosis [Radlex concept]
- primary biliary cirrhosis [SNOMED Notion]
ICD-10 Mapping
- Primary biliary cirrhosis [ICD-10 Sub-category]

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