" /> Primary Biliary Cirrhosis - CISMeF





Preferred Label : Primary Biliary Cirrhosis;

NCIt synonyms : Chronic Non-Suppurative Destructive Cholangitis; Primary Biliary Cirrhosis (PBC);

NCIt related terms : Primary Biliary Cholangitis;

NCIt definition : An autoimmune inflammatory disorder characterized by destruction of the small intrahepatic bile ducts. It affects predominantly females and it may lead to cirrhosis and liver failure. Patients have antimitochondrial and antinuclear antibodies in the peripheral blood.;

Codes from synonyms : K74.3;

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28/07/2025


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