ICD-11 code : EA94;
Preferred Label : Pityriasis rubra pilaris;
ICD-11 definition : Pityriasis rubra pilaris (PRP) is the name given to a group of clinically similar
papulosquamous dermatoses of unknown aetiology. They initially present with erythematous,
hyperkeratotic perifollicular papules, which tend to coalesce into plaques, but may
progress to erythroderma, particularly in adults. The distribution, age of onset and
speed of onset differ markedly between patients and these differences have been used
to classify PRP into a number of clinically distinct subtypes.;
ICD-11 synonym : PRP - [pityriasis rubra pilaris];
ICD-11 acronym : PRP;
ICD-11 inclusion : Devergie's disease;
Origin ID : 2048594962;
UMLS CUI : C0032027;
Automatic exact mappings (from CISMeF team)
Currated CISMeF NLP mapping
ICD-10 Mapping
Semantic type(s)
UMLS correspondences (same concept)
Pityriasis rubra pilaris (PRP) is the name given to a group of clinically similar
papulosquamous dermatoses of unknown aetiology. They initially present with erythematous,
hyperkeratotic perifollicular papules, which tend to coalesce into plaques, but may
progress to erythroderma, particularly in adults. The distribution, age of onset and
speed of onset differ markedly between patients and these differences have been used
to classify PRP into a number of clinically distinct subtypes.